ICD-10 Chapter VI: Diseases of the nervous system

G00-G99 - Diseases of the nervous system

(G00-G09) Inflammatory diseases of the central nervous system

• (G00) Bacterial meningitis, not elsewhere classified
  • (G00.0) Haemophilus meningitis
  • (G00.1) Pneumococcal meningitis
  • (G00.2) Streptococcal meningitis
  • (G00.3) Staphylococcal meningitis
  • (G00.8) Other bacterial meningitis
    • Meningitis due to Escherichia coli
    • Meningitis due to Friedländer bacillus
    • Meningitis due to Klebsiella
  • (G00.9) Bacterial meningitis, unspecified

• (G01) Meningitis in bacterial diseases classified elsewhere
• (G02) Meningitis in other infectious and parasitic diseases classified elsewhere

• (G03) Meningitis due to other and unspecified causes
  • (G03.0) Nonpyogenic meningitis
  • (G03.1) Chronic meningitis
  • (G03.2) Benign recurrent meningitis (Mollaret)
  • (G03.8) Meningitis due to other specified causes
  • (G03.9) Meningitis, unspecified
    • Arachnoiditis (spinal) NOS

• (G04) Encephalitis, myelitis and encephalomyelitis
  • (G04.0) Acute disseminated encephalitis
  • (G04.1) Tropical spastic paraplegia
  • (G04.2) Bacterial meningoencephalitis and meningomyelitis, not elsewhere classified
  • (G04.8) Other encephalitis, myelitis and encephalomyelitis
  • (G04.9) Encephalitis, myelitis and encephalomyelitis, unspecified

• (G05) Encephalitis, myelitis and encephalomyelitis in diseases classified elsewhere
• (G06) Intracranial and intraspinal abscess and granuloma
• (G07) Intracranial and intraspinal abscess and granuloma in diseases classified elsewhere
• (G08) Intracranial and intraspinal phlebitis and thrombophlebitis
• (G09) Sequelae of inflammatory diseases of central nervous system

(G10-G13) Systemic atrophies primarily affecting the central nervous system

• (G10) Huntington's disease

• (G11) Hereditary ataxia
  • (G11.0) Congenital nonprogressive ataxia
  • (G11.1) Early-onset cerebellar ataxia
    • Early-onset cerebellar ataxia with essential tremor
    • Early-onset cerebellar ataxia with myoclonus (Hunt's ataxia)
    • Early-onset cerebellar ataxia with retained tendon reflexes
    • Friedreich's ataxia (autosomal recessive)
    • X-linked recessive spinocerebellar ataxia
  • (G11.2) Late-onset cerebellar ataxia
  • (G11.3) Cerebellar ataxia with defective DNA repair
    • Ataxia telangiectasia (Louis-Bar)
  • (G11.4) Hereditary spastic paraplegia
  • (G11.8) Other hereditary ataxias
  • (G11.9) Hereditary ataxia, unspecified

• (G12) Spinal muscular atrophy and related syndromes
  • (G12.0) Werdnig-Hoffman disease (Type 1)
  • (G12.1) Other inherited spinal muscular atrophy
    • Progressive bulbar palsy of childhood (Fazio-Londe)
    • Kugelberg-Welander disease (Type 3)
  • (G12.2) Motor neuron disease
    • Familial motor neuron disease
    • Amyotrophic lateral sclerosis
    • Primary lateral sclerosis
    • Progressive bulbar palsy
    • Progressive spinal muscular atrophy

• (G13) Systemic atrophies primarily affecting central nervous system in diseases classified elsewhere
  • (G13.0) Paraneoplastic neuromyopathy and neuropathy
  • (G13.1) Other systemic atrophy primarily affecting central nervous system in neoplastic disease
    • Paraneoplastic limbic encephalopathy
  • (G13.2) Systemic atrophy primarily affecting central nervous system in myxoedema
  • (G13.8) Systemic atrophy primarily affecting central nervous system in other diseases classified elsewhere

(G20-G26) Extrapyramidal and movement disorders

• (G20) Parkinson's disease

• (G21) Secondary parkinsonism
  • (G21.0) Malignant neuroleptic syndrome
  • (G21.3) Postencephalitic parkinsonism

• (G22) Parkinsonism in diseases classified elsewhere

• (G23) Other degenerative diseases of basal ganglia
  • (G23.0) Hallervorden-Spatz disease
  • (G23.1) Progressive supranuclear ophthalmoplegia (Steele-Richardson-Olszewski)
  • (G23.2) Striatonigral degeneration
  • (G23.8) Other specified degenerative diseases of basal ganglia
  • (G23.9) Degenerative disease of basal ganglia, unspecified

• (G24) Dystonia
  • (G24.0) Drug-induced dystonia
  • (G24.1) Idiopathic familial dystonia
  • (G24.2) Idiopathic nonfamilial dystonia
  • (G24.3) Spasmodic torticollis
  • (G24.4) Idiopathic orofacial dystonia
    • Orofacial dyskinesia
  • (G24.5) Blepharospasm
  • (G24.8) Other dystonia
  • (G24.9) Dystonia, unspecified
    • Dyskinesia NOS

• (G25) Other extrapyramidal and movement disorders
  • (G25.0) Essential tremor
  • (G25.1) Drug-induced tremor
  • (G25.2) Other specified forms of tremor
  • (G25.3) Myoclonus
  • (G25.4) Drug-induced chorea
  • (G25.5) Other chorea
  • (G25.6) Drug-induced tics and other tics of organic origin
  • (G25.8) Other specified extrapyramidal and movement disorders
    • Restless legs syndrome
    • Stiff-man syndrome
  • (G25.9) Extrapyramidal and movement disorder, unspecified

• (G26) Extrapyramidal and movement disorders in diseases classified elsewhere

(G30-G32) Other degenerative diseases of the nervous system

• (G30) Alzheimer's disease

• (G31) Other degenerative diseases of nervous system, not elsewhere classified
  • (G31.0) Circumscribed brain atrophy
    • Pick's disease
  • (G31.1) Senile degeneration of brain, not elsewhere classified
  • (G31.2) Degeneration of nervous system due to alcohol
  • (G31.8) Other specified degenerative diseases of nervous system
    • Grey-matter degeneration (Alpers)
    • Lewy body dementia
    • Subacute necrotizing encephalopathy (Leigh)
  • (G31.9) Degenerative disease of nervous system, unspecified

• (G32) Other degenerative disorders of nervous system in diseases classified elsewhere
  • (G32.0) Subacute combined degeneration of spinal cord in diseases classified elsewhere
  • (G32.8) Other specified degenerative disorders of nervous system in diseases classified elsewhere

(G35-G37) Demyelinating diseases of the central nervous system

• (G35) Multiple sclerosis

• (G36) Other acute disseminated demyelination
  • (G36.0) Neuromyelitis optica (Devic)
  • (G36.1) Acute and subacute haemorrhagic leukoencephalitis (Hurst)
  • (G36.8) Other specified acute disseminated demyelination
  • (G36.9) Acute disseminated demyelination, unspecified

• (G37) Other demyelinating diseases of central nervous system
  • (G37.0) Diffuse sclerosis
  • (G37.1) Central demyelination of corpus callosum
  • (G37.2) Central pontine myelinolysis
  • (G37.3) Acute transverse myelitis in demyelinating disease of central nervous system
  • (G37.4) Subacute necrotizing myelitis
  • (G37.5) Concentric sclerosis (Baló)
  • (G37.8) Other specified demyelinating diseases of central nervous system
  • (G37.9) Demyelinating disease of central nervous system, unspecified

(G40-G47) Episodic and paroxysmal disorders

• (G40) Epilepsy
  • (G40.0) Localization-related (focal)(partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset
  • (G40.1) Localization-related (focal)(partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures
  • (G40.2) Localization-related (focal)(partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures
  • (G40.3) Generalized idiopathic epilepsy and epileptic syndromes
    • Benign:
      • myoclonic epilepsy in infancy
      • neonatal convulsions (familial)
    • Childhood absence epilepsy (pyknolepsy)
    • Epilepsy with grand mal seizures on awakening
    • Juvenile:
      • absence epilepsy
      • myoclonic epilepsy (impulsive petit mal)
    • Nonspecific epileptic seizures:
      • atonic
      • clonic
      • myoclonic
      • tonic
      • tonic-clonic
  • (G40.4) Other generalized epilepsy and epileptic syndromes
    • Epilepsy with:
      • myoclonic absences
      • myoclonic-astatic seizures
    • Infantile spasms
    • Lennox-Gastaut syndrome
    • Salaam attacks
    • Symptomatic early myoclonic encephalopathy
    • West's syndrome
  • (G40.5) Special epileptic syndromes
    • Epilepsia partialis continua (Kozhevnikof)
  • (G40.6) Grand mal seizures, unspecified (with or without petit mal)
  • (G40.7) Petit mal, unspecified, without grand mal seizures
  • (G40.8) Other epilepsy
    • Epilepsies and epileptic syndromes undetermined as to whether they are focal or generalized
  • (G40.9) Epilepsy, unspecified

• (G41) Status epilepticus
  • (G41.0) Grand mal status epilepticus
  • (G41.1) Petit mal status epilepticus
  • (G41.2) Complex partial status epilepticus
  • (G41.8) Other status epilepticus
  • (G41.9) Status epilepticus, unspecified

• (G43) Migraine
  • (G43.0) Migraine without aura (common migraine)
  • (G43.1) Migraine with aura (classical migraine)
  • (G43.2) Status migrainosus
  • (G43.3) Complicated migraine
  • (G43.8) Other migraine
  • (G43.9) Migraine, unspecified

• (G44) Other headache syndromes
  • (G44.0) Cluster headache syndrome
  • (G44.1) Vascular headache, not elsewhere classified
  • (G44.2) Tension-type headache
  • (G44.3) Chronic post-traumatic headache
  • (G44.4) Drug-induced headache, not elsewhere classified
  • (G44.8) Other specified headache syndromes

• (G45) Transient cerebral ischaemic attacks and related syndromes
  • (G45.0) Vertebro-basilar artery syndrome
  • (G45.1) Carotid artery syndrome (hemispheric)
  • (G45.2) Multiple and bilateral precerebral artery syndromes
  • (G45.3) Amaurosis fugax
  • (G45.4) Transient global amnesia
  • (G45.8) Other transient cerebral ischaemic attacks and related syndromes
  • (G45.9) Transient cerebral ischaemic attack, unspecified

• (G46) Vascular syndromes of brain in cerebrovascular diseases
  • (G46.0) Middle cerebral artery syndrome
  • (G46.1) Anterior cerebral artery syndrome
  • (G46.2) Posterior cerebral artery syndrome
  • (G46.3) Brain stem stroke syndrome
    • Benedikt syndrome
    • Claude syndrome
    • Foville syndrome
    • Millard-Gubler syndrome
    • Wallenberg syndrome
    • Weber syndrome
  • (G46.4) Cerebellar stroke syndrome
  • (G46.5) Pure motor lacunar syndrome
  • (G46.6) Pure sensory lacunar syndrome
  • (G46.7) Other lacunar syndromes
  • (G46.8) Other vascular syndromes of brain in cerebrovascular diseases

• (G47) Sleep disorders
  • (G47.0) Disorders of initiating and maintaining sleep (insomnias)
  • (G47.1) Disorders of excessive somnolence (hypersomnias)
  • (G47.2) Disruptions in circadian rhythm including jet lag
  • (G47.3) Sleep apnoea
  • (G47.4) Narcolepsy and cataplexy

(G50-G59) Nerve, nerve root and plexus disorders

• (G50) Disorders of trigeminal nerve (V)
  • (G50.0) Trigeminal neuralgia

• (G51) Facial nerve disorders (VII)
  • (G51.0) Bell's palsy
    • Facial palsy
  • (G51.1) Geniculate ganglionitis
  • (G51.2) Melkersson's syndrome
    • Melkersson-Rosenthal syndrome
  • (G51.3) Clonic hemifacial spasm
  • (G51.4) Facial myokymia
  • (G51.8) Other disorders of facial nerve
  • (G51.8) Disorder of facial nerve, unspecified

• (G52) Disorders of other cranial nerves
  • (G52.0) Disorders of olfactory nerve (I)
  • (G52.1) Disorders of glossopharyngeal nerve (IX)
  • (G52.2) Disorders of vagus nerve (X)
  • (G52.3) Disorders of hypoglossal nerve (XII)
  • (G52.7) Disorders of multiple cranial nerves
  • (G52.8) Disorders of other specified cranial nerves
  • (G52.9) Cranial nerve disorder, unspecified

• (G53) Cranial nerve disorders in diseases classified elsewhere

• (G54) Nerve root and plexus disorders
  • (G54.0) Brachial plexus disorders
    • Thoracic outlet syndrome
  • (G54.1) Lumbosacral plexus disorders
  • (G54.2) Cervical root disorders, not elsewhere classified
  • (G54.3) Thoracic root disorders, not elsewhere classified
  • (G54.4) Lumbosacral root disorders, not elsewhere classified
  • (G54.5) Neuralgic amyotrophy
    • Parsonage-Aldren-Turner syndrome
  • (G54.6) Phantom limb syndrome with pain
  • (G54.7) Phantom limb syndrome without pain
• (G55) Nerve root and plexus compressions in diseases classified elsewhere
• (G56) Mononeuropathies of upper limb
  • (G56.0) Carpal tunnel syndrome
  • (G56.4) Causalgia
• (G57) Mononeuropathies of lower limb
  • (G57.0) Lesion of sciatic nerve
  • (G57.1) Meralgia paraesthetica
  • (G57.2) Lesion of femoral nerve
  • (G57.3) Lesion of lateral popliteal nerve
  • (G57.4) Lesion of medial popliteal nerve
  • (G57.5) Tarsal tunnel syndrome
  • (G57.6) Lesion of plantar nerve
    • Morton's metatarsalgia
  • (G57.8) Other mononeuropathies of lower limb
  • (G57.9) Mononeuropathy of lower limb, unspecified

• (G58) Other mononeuropathies
  • (G58.0) Intercostal neuropathy
  • (G58.7) Mononeuritis multiplex
  • (G58.8) Other specified mononeuropathies
  • (G58.9) Mononeuropathy, unspecified

• (G59) Mononeuropathy in diseases classified elsewhere

(G60-G64) Polyneuropathies and other disorders of the peripheral nervous system

• (G60) Hereditary and idiopathic neuropathy
  • (G60.0) Hereditary motor and sensory neuropathy
    • Charcot-Marie-Tooth disease
    • Déjerine-Sottas disease
    • Hereditary motor and sensory neuropathy, types I-IV
    • Hypertrophic neuropathy of infancy
    • Peroneal muscular atrophy (axonal type)(hypertrophic type)
    • Roussy-Lévy syndrome
  • (G60.1) Refsum's disease
  • (G60.2) Neuropathy in association with hereditary ataxia
  • (G60.3) Idiopathic progressive neuropathy
  • (G60.8) Other hereditary and idiopathic neuropathies
    • Morvan's disease
    • Nelaton's syndrome
    • Sensory neuropathy
  • (G60.9) Hereditary and idiopathic neuropathy, unspecified

• (G61) Inflammatory polyneuropathy
  • (G61.0) Guillain-Barré syndrome
  • (G61.1) Serum neuropathy
  • (G61.8) Other inflammatory polyneuropathies
  • (G61.9) Inflammatory polyneuropathy, unspecified

• (G62) Other polyneuropathies
  • (G62.0) Drug-induced polyneuropathy
  • (G62.1) Alcoholic polyneuropathy
  • (G62.2) Polyneuropathy due to other toxic agents
  • (G62.8) Other specified polyneuropathies
  • (G62.9) Polyneuropathy, unspecified
    • Neuropathy NOS

• (G63) Polyneuropathy in diseases classified elsewhere
• (G64) Other Disorders of peripheral nervous system

(G70-G73) Diseases of myoneural junction and muscle

• (G70) Myasthenia gravis and other myoneural disorders
  • (G70.0) Myasthenia gravis
  • (G70.1) Toxic myoneural disorders
  • (G70.2) Congenital and developmental myasthenia
• (G71) Primary disorders of muscles
  • (G71.0) Muscular dystrophy
    • benign muscular dystrophy (Becker muscular dystrophy)
    • benign scapuloperoneal muscular dystrophy with early contractures (Emery-Dreifuss muscular dystrophy)
    • distal muscular dystrophy
    • facioscapulohumeral muscular dystrophy
    • limb-girdle muscular dystrophy
    • ocular muscular dystrophy
    • oculopharyngeal muscular dystrophy
    • scapuloperoneal muscular dystrophy
    • severe muscular dystrophy (Duchenne muscular dystrophy)
  • (G71.1) Myotonic disorders
    • Dystrophia myotonica (Steinert)
    • chondrodystrophic myotonia
    • drug-induced myotonia
    • symptomatic myotonia
    • Myotonia congenita - NOS:
    • Myotonia congenita - dominant (Thomsen)
    • Myotonia congenita - recessive (Becker)
    • Neuromyotonia (Isaacs)
    • Paramyotonia congenita
    • Pseudomyotonia
  • (G71.2) Congenital myopathies, including:
    • Central core disease
    • Congenital muscular dystrophy
    • Centronuclear myopathy
    • Fibre-type disproportion
    • Minicore disease
    • Multicore disease
    • Myotubular myopathy
    • Nemaline myopathy
  • (G71.3) Mitochondrial myopathy, not elsewhere classified
• (G72) Other myopathies
  • (G72.0) Drug-induced myopathy
  • (G72.1) Alcoholic myopathy
  • (G72.2) Myopathy due to other toxic agents
  • (G72.3) Periodic paralysis
    • Hypokalemic periodic paralysis
    • Hyperkalemic periodic paralysis
• (G73) Disorders of myoneural junction and muscle in diseases classified elsewhere
  • (G73.0) Myasthenic syndromes in endocrine diseases
  • (G73.1) Eaton-Lambert syndrome
  • (G73.2) Other myasthenic syndromes in neoplastic disease
  • (G73.3) Myasthenic syndromes in other diseases classified elsewhere
  • (G73.4) Myopathy in infectious and parasitic diseases classified elsewhere
  • (G73.5) Myopathy in endocrine diseases
  • (G73.6) Myopathy in metabolic diseases
  • (G73.7) Myopathy in other diseases classified elsewhere

(G80-G83) Cerebral palsy and other paralytic syndromes

• (G80) Cerebral palsy
  • (G80.0) Spastic quadriplegic cerebral palsy
  • (G80.1) Spastic diplegic cerebral palsy
  • (G80.2) Spastic hemiplegic cerebral palsy
  • (G80.3) Dyskinetic cerebral palsy
  • (G80.4) Ataxic cerebral palsy
  • (G80.8) Other cerebral palsy
  • (G80.9) Cerebral palsy, unspecified

• (G81) Hemiplegia
  • (G81.0) Flaccid hemiplegia
  • (G81.1) Spastic hemiplegia
  • (G81.9) Hemiplegia, unspecified

• (G82) Paraplegia and tetraplegia
  • (G82.0) Flaccid paraplegia
  • (G82.1) Spastic paraplegia
  • (G82.2) Paraplegia, unspecified
    • Paralysis of both lower limbs NOS
    • Paraplegia (lower) NOS
  • (G82.3) Flaccid tetraplegia
  • (G82.4) Spastic tetraplegia
  • (G82.5) Tetraplegia, unspecified
    • Quadriplegia NOS

• (G83) Other paralytic syndromes
  • (G83.0) Diplegia of upper limbs
  • (G83.1) Monoplegia of lower limb
  • (G83.2) Monoplegia of upper limb
  • (G83.3) Monoplegia, unspecified
  • (G83.4) Cauda equina syndrome
  • (G83.8) Other specified paralytic syndromes
    • Todd's paralysis (postepileptic)
  • (G83.9) Paralytic syndrome, unspecified

(G90-G99) Other disorders of the nervous system

• (G90) Disorders of autonomic nervous system
  • (G90.0) Idiopathic peripheral autonomic neuropathy
  • (G90.1) Familial dysautonomia (Riley-Day)
  • (G90.2) Horner's syndrome
  • (G90.3) Multi-system degeneration
  • (G90.8) Other disorders of autonomic nervous system
  • (G90.9) Disorder of autonomic nervous system, unspecified

• (G91) Hydrocephalus
• (G92) Toxic encephalopathy

• (G93) Other disorders of brain
  • (G93.0) Cerebral cysts
  • (G93.1) Anoxic brain damage, not elsewhere classified
  • (G93.2) Benign intracranial hypertension
  • (G93.3) Postviral fatigue syndrome
  • (G93.4) Encephalopathy, unspecified
  • (G93.5) Compression of brain
  • (G93.6) Cerebral oedema
  • (G93.7) Reye's syndrome
  • (G93.8) Other specified disorders of brain
    • Postradiation encephalopathy
  • (G93.9) Disorder of brain, unspecified

• (G94) Other disorders of brain in diseases classified elsewhere

• (G95) Other diseases of spinal cord
  • (G95.0) Syringomyelia and syringobulbia
  • (G95.1) Vascular myelopathies
  • (G95.2) Cord compression, unspecified
  • (G95.8) Other specified diseases of spinal cord
  • (G95.9) Disease of spinal cord, unspecified
    • Myelopathy NOS

• (G96) Other disorders of central nervous system
• (G97) Postprocedural disorders of nervous system, not elsewhere classified
• (G98) Other disorders of nervous system, not elsewhere classified
• (G99) Other disorders of nervous system in diseases classified elsewhere

See also

• List of ICD-10 codes
• International Statistical Classification of Diseases and Related Health Problems