Noncompaction cardiomyopathy: Difference between revisions

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{{CMG}}; '''Associate Editors-In-Chief:''' {{CZ}}
{{CMG}}; '''Associate Editors-In-Chief:''' {{CZ}}


'''''Synonyms and keywords:''''' left ventricular noncompaction, LVNC, NCC, spongiform cardiomyopathy
'''''Synonyms and keywords:''''' left ventricular noncompaction, LVNC, NCC, spongiform cardiomyopathy, (Isolated) noncompaction of the ventricular myocardium, (I)NVM, non-compaction of the left ventricular myocardium, left ventricular hypertrabeculation, spongy myocardium.


==[[Noncompaction cardiomyopathy overview|Overview]]==
==[[Noncompaction cardiomyopathy overview|Overview]]==


==[[Noncompaction cardiomyopathy historical perspective|Historical Perspective]]==
==[[Noncompaction cardiomyopathy historical perspective|Historical Perspective]]==
==[[Noncompaction cardiomyopathy classification|Classification System and Nomenclature]]==


==[[Noncompaction cardiomyopathy pathophysiology|Pathophysiology]]==
==Pathophysiology==


==[[Noncompaction cardiomyopathy epidemiology and demographics|Epidemiology]]==
[[Noncompaction cardiomyopathy embryology|Embryology]] | [[Noncompaction cardiomyopathy histology|Histology]] | [[Noncompaction cardiomyopathy genetics|Genetics]] | [[Noncompaction cardiomyopathy left ventricular dysfunction|Left ventricular dysfunction]] | [[Noncompaction cardiomyopathy thromboembolism|Thromboembolism]] | [[Noncompaction cardiomyopathy neuromuscular disorders|Neuromuscular disorders]]
 
==[[Noncompaction cardiomyopathy epidemiology and demographics|Epidemiology and Demographics]]==
 
==[[Noncompaction cardiomyopathy screening|Screening]]==


==[[Noncompaction_cardiomyopathy_natural_history|Natural History, Complications & Prognosis]]==
==[[Noncompaction_cardiomyopathy_natural_history|Natural History, Complications & Prognosis]]==


==[[Noncompaction_cardiomyopathy_differential diagnosis|Differentiating Noncompaction Cardiomyopathy other Diseases]]==
==[[Noncompaction_cardiomyopathy_differential diagnosis|Differentiating Noncompaction Cardiomyopathy from other Diseases]]==


==Diagnosis==
==Diagnosis==
===[[Noncompaction cardiomyopathy history and symptoms|Symptoms]]===
[[Noncompaction cardiomyopathy history and symptoms|History & Symptoms]] | [[Noncompaction cardiomyopathy physical examination|Physical Examination]] | [[Noncompaction cardiomyopathy laboratory studies|Laboratory Studies]] | [[Noncompaction cardiomyopathy genetic testing|Genetic Testing]] |
 
[[Noncompaction cardiomyopathy electrocardiogram|Electrocardiogram]] | [[Noncompaction cardiomyopathy chest x ray|Chest X Ray]] | [[Noncompaction cardiomyopathy echocardiography or ultrasound|Echocardiography]] | [[Noncompaction cardiomyopathy MRI|MRI]] | [[Noncompaction cardiomyopathy CT|CT]] | [[Noncompaction cardiomyopathy other diagnostic studies|Biopsy]]
===[[Noncompaction cardiomyopathy echocardiography|Echocardiography]]===
 
 


==Management==
==Management==
The management of NCC is similar to that of other cardiomyopathies and includes the use of [[angiotensin-converting enzyme|ACE inhibitors]], [[Beta blocker|beta blockers]] and [[aspirin]]. Implantation of an [[automatic internal cardiac defibrillator]] [[AICD]] may be appropriate in patients who are deemed to be at increased risk of [[sudden cardiac death]].  A small study from the Netherlands identified young females with [[premature ventricular contractions]] ([[PVCs]]) at risk of [[sudden death]]<ref>[http://spo.escardio.org/eslides/view.aspx?eevtid=33&fp=4147]</ref>.
[[Noncompaction cardiomyopathy medical therapy|Medical Therapy]] | [[Noncompaction cardiomyopathy surgery|Surgery]]
 
In severe NCC cases, in which severe [[heart failure]] has developed, a [[heart transplant]] may be necessary.
 
==Source==
*{{cite web | title=Left Ventriuclar noncompaction| work=Orphanet| url=http://www.orpha.net/data/patho/GB/uk-LVNC.pdf}}


==See also==
==See also==
[[Cardiomyopathy]], [[Barth syndrome]], [[Emery-Dreifuss muscular dystrophy]], [[myotubular myopathy]], genes responsible for NCC are located also in the area that cause these conditions.


[[Barth syndrome]], [[Emery-Dreifuss muscular dystrophy]], [[myotubular myopathy]], genes responsible for NCC are located also in the area that cause these conditions.
{{Circulatory system pathology}}


==References==
{{Reflist|2}}
==Additional Resources==
*{{cite web | title=Left Ventricular Non-compaction | work=Baylor College of Medicine| url=http://www.bcm.edu/pediatrics/index.cfm?realm=99992426&This_Template=LVNC}}
*{{cite web | title=Contemporary Definitions and Classification of the Cardiomyopathies| work=American Heart Association Scientific Statement | url=http://circ.ahajournals.org/cgi/content/full/113/14/1807}}
{{Circulatory system pathology}}
{{SIB}}
[[Category:Cardiology]]
[[Category:Cardiology]]
[[Category:Cardiomyopathy]]
[[Category:Cardiomyopathy]]

Latest revision as of 16:04, 7 August 2011

Noncompaction cardiomyopathy

Noncompaction Cardiomyopathy Microchapters

Home

Patient Info

Overview

Historical Perspective

Classification & Nomenclature

Pathophysiology

Genetics
Embryology
Histology
Left Ventricular Dysfunction
Arrhythmias
Thromboembolism
Neuromuscular Disorders

Epidemiology & Demographics

Screening

Natural History, Complications & Prognosis

Differentiating Noncompaction Cardiomyopathy from other Diseases

Diagnosis

History & Symptoms

Physical Examination

Laboratory Studies

Genetic Testing

Electrocardiogram

Holter Monitoring

Chest X Ray

MRI

CT

Echocardiography

Biopsy

Treatment

Medical Therapy

Surgery

Noncompaction cardiomyopathy On the Web

Most recent articles

Most cited articles

Review articles

CME Programs

Powerpoint slides

Images

Ongoing Trials at Clinical Trials.gov

US National Guidelines Clearinghouse

NICE Guidance

FDA on Noncompaction cardiomyopathy

CDC on Noncompaction cardiomyopathy

Noncompaction cardiomyopathy in the news

Blogs on Noncompaction cardiomyopathy

Directions to Hospitals Treating Type page name here

Risk calculators and risk factors for Noncompaction cardiomyopathy

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editors-In-Chief: Cafer Zorkun, M.D., Ph.D. [2]

Synonyms and keywords: left ventricular noncompaction, LVNC, NCC, spongiform cardiomyopathy, (Isolated) noncompaction of the ventricular myocardium, (I)NVM, non-compaction of the left ventricular myocardium, left ventricular hypertrabeculation, spongy myocardium.

Overview

Historical Perspective

Classification System and Nomenclature

Pathophysiology

Embryology | Histology | Genetics | Left ventricular dysfunction | Thromboembolism | Neuromuscular disorders

Epidemiology and Demographics

Screening

Natural History, Complications & Prognosis

Differentiating Noncompaction Cardiomyopathy from other Diseases

Diagnosis

History & Symptoms | Physical Examination | Laboratory Studies | Genetic Testing | Electrocardiogram | Chest X Ray | Echocardiography | MRI | CT | Biopsy

Management

Medical Therapy | Surgery

See also

Cardiomyopathy, Barth syndrome, Emery-Dreifuss muscular dystrophy, myotubular myopathy, genes responsible for NCC are located also in the area that cause these conditions.


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