Desmoid tumor classification

Desmoid tumor Microchapters
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Differentiating Desmoid tumor from other Diseases
Epidemiology and Demographics
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Natural History, Complications and Prognosis
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Case #1

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor(s)-in-Chief: Sara Mohsin, M.D.[2]Faizan Sheraz, M.D. [3]

Overview

Based on the etiology, desmoid tumors may be classified as abdominal, intra-abdominal, extra-abdominal, multiple familial, associated with Gardner syndrome and associated with Turcot syndrome.

Classification

• Based on the etiology, desmoid tumors may be classified as:

Classification	Features
Abdominal	Most commonly arise from anterior abdominal wall with 50% incidence
Extraabdominal	Desmoid tumors found in other body regions most often including: Shoulder girdle Upper arms Upper legs Hip/buttock region Trunk Head Neck Breast (history of breast cancer/breast surgery)
Intraabdominal	Arise from the tissue that connects the abdominal organs, involving: Mesentery Retroperitoneum Bowel Predominantly present in FAP patients
Multiple Familial	Hereditary predisposition
Gardner Syndrome Associated	Soft tissue tumors Osteoma
Turcot Syndrome Associated	Neural tumors