Rhabdomyoma medical therapy

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Nima Nasiri, M.D.[2]

Overview

Rhabdomyoma is a benign tumor of striated muscle. Rhabdomyomas are rare and can be classified into cardiac type and extracardiac type.The most common primary benign pediatric tumor of the heart is cardiac rhabdomyoma which can be seen mainly in fetal life and children, second most common primary benign cardiac tumor in children is fibroma. Most tumors regress spontaneously, prognosis depends on the location of tumor and size. Cardiac rhabdomyoma is strongly associated with tuberous sclerosis.

Treatment

Medical Therapy

Adult rhabdomyoma

  • Patients with laryngeal rhabdomyoma need immediate care such as nasal oxygen, intravenous fluids and if respiratory distress develops intubation before admission for surgery and surgical excision. [4]
  • Patients with adult rhabdomyoma and shortness of breath should restrain from activities which exacerbate their breathing difficulty.

Cardiac rhabdomyoma

Genital rhabdomyoma

References

  1. Tiberio D, Franz DN, Phillips JR (2011). "Regression of a cardiac rhabdomyoma in a patient receiving everolimus". Pediatrics. 127 (5): e1335–7. doi:10.1542/peds.2010-2910. PMID 21464184.
  2. Wagner R, Riede FT, Seki H, Hornemann F, Syrbe S, Daehnert I; et al. (2015). "Oral Everolimus for Treatment of a Giant Left Ventricular Rhabdomyoma in a Neonate-Rapid Tumor Regression Documented by Real Time 3D Echocardiography". Echocardiography. 32 (12): 1876–9. doi:10.1111/echo.13015. PMID 26199144.
  3. Öztunç F, Atik SU, Güneş AO (October 2015). "Everolimus treatment of a newborn with rhabdomyoma causing severe arrhythmia". Cardiol Young. 25 (7): 1411–4. doi:10.1017/S1047951114002261. PMID 26339757.
  4. Amelia Souza A, de Araújo VC, Passador Santos F, Ferreira Martinez E, de Menezes Filho JF, Soares de Araujo N, Soares AB (2013). "Intraoral adult rhabdomyoma: a case report". Case Rep Dent. 2013: 741548. doi:10.1155/2013/741548. PMC 3833031. PMID 24288631.
  5. Martínez-García A, Michel-Macías C, Cordero-González G, Escamilla-Sánchez KI, Aguinaga-Ríos M, Coronado-Zarco A, Cardona-Pérez JA (July 2018). "Giant left ventricular rhabdomyoma treated successfully with everolimus: case report and review of literature". Cardiol Young. 28 (7): 903–909. doi:10.1017/S1047951118000598. PMID 29759095.
  6. Lu DY, Chang S, Cook H, Alizadeh Y, Karam AK, Moatamed NA, Dry SM (April 2012). "Genital rhabdomyoma of the urethra in an infant girl". Hum. Pathol. 43 (4): 597–600. doi:10.1016/j.humpath.2011.06.012. PMID 21992817.
  7. Dodat H, Paulhac JB, Macabeo V, Bouvier R (1987). "[Benign tumors of the posterior urethra in children. Apropos of an unusual case of rhabdomyoma of fetal type]". J Urol (Paris) (in French). 93 (1): 43–6. PMID 3031168.

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