Adiposogenital dystrophy
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| Adiposogenital dystrophy Classification and external resources | |
| ICD-10 | E23.6 |
|---|---|
| ICD-9 | 253.8 |
| DiseasesDB | 29318 |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Phone:617-632-7753
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Adiposogenital dystrophy is a medical condition.
Presentation
It is characterized by:
- Feminine obesity
- Growth retardation and retarded sexual development, atrophy or hypoplasia of the gonads, and altered secondary sex characteristics,
- headaches
- mental retardation, problems with vision
- polyuria, polydipsia.
It is usually associated with tumours of the hypothalamus, causing increased appetite and depressed secretion of gonadotropin. It seems to affect males mostly.
Many overweight children may appear to have the disorder because of the concurrence of obesity and retarded sexual development; these children have no endocrine disturbances, however, and they mature normally after delayed puberty.
Synonyms
It has several other names:[1]
- Babinski-Fröhlich syndrome[2] (named after Joseph Babinski[3] and Alfred Fröhlich,[4] but probably first described by Morgagni). (It was given its name by Harvey Cushing.)[5]
- Froelich's syndrome
- Frölich's Syndrome
- Hypothalamic Infantilism-Obesity
- Launois-Cleret Syndrome
- Sexual Infantilism
See also
- Prader-Willi syndrome, to which it might resemble. However, this is a genetic disorder.
References
- ↑ National Organisation for Rare Disorders - Froelich's syndrome
- ↑ synd/1792 at Who Named It - Babinski-Fröchlich syndrome
- ↑ J. F. Babinski. Tumeur du corps pituitaire sans acromégalie et avec arrêt de développement des organes génitaux. Revue neurologique, Paris, 1900, 8: 531-535.
- ↑ A. Fröhlich. Ein Fall von Tumor der Hypophysis cerebri ohne Akromegalie. Wiener klinische Rundschau, 1901, 15: 833-836; 906-908.
- ↑ Zárate A, Saucedo R (2007). "[The adiposogenital distrophy or Frohlich syndrome and the beginning of the concept of neuroendocrinology]" (in Spanish; Castilian). Gac Med Mex 143 (4): 349–50. PMID 17969845.
Acknowledgement and Attribution Regarding Sources of Content
Some of the initial content on this page may be incorporated in part from copyleft sources in the public domain including wikis such as Wikipedia and AskDrWiki. Drug information for patients came from the The National Library of Medicine. Infectious disease information may have come from the Centers for Disease Control (CDC). Differential Diagnoses are drawn from clinicians as well as an amalgamation of 3 sources: 1.The Disease Database; 2. Kahan, Scott, Smith, Ellen G. In A Page: Signs and Symptoms. Malden, Massachusetts: Blackwell Publishing, 2004:3; 3. Sailer, Christian, Wasner, Susanne. Differential Diagnosis Pocket. Hermosa Beach, CA: Borm Bruckmeir Publishing LLC, 2002:7 .
