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'''For patient information click [[{{PAGENAME}} (patient information)|here]]'''
__NOTOC__
{{Infobox_Disease
{{Infobox_Disease
  | Name          = {{PAGENAME}}
  | Name          = Hereditary pancreatitis
  | Image          =  
  | Image          = Blausen 0699 PancreasAnatomy2.png
  | Caption        =  
  | Caption        = Pancreas<ref><https://en.wikipedia.org/wiki/Pancreas#/media/File:Blausen_0699_PancreasAnatomy2.png></ref>
| DiseasesDB    = 30026
| ICD10          =
| ICD9          =
| ICDO          =
| OMIM          = 167800
| MedlinePlus    =
| eMedicineSubj  =
| eMedicineTopic =
| MeshID        =
}}
}}
{{SI}}
{{Hereditary pancreatitis}}
{{CMG}}
'''For patient information, click [[Xyz (patient information)|here]]'''


{{CMG}}; {{AE}}: {{IQ}}


{{SK}} Hereditary chronic pancreatitis


==Overview==
==[[Hereditary pancreatitis overview|Overview]]==
'''Hereditary Pancreatitis''' is a genetic disease affecting enzyme production in the pancreas. In the pancreas, a genetic mutation causes the enzyme [[trypsinogen]] to be made in a way which renders it resistant to inactivation through [[autolysis]]. Normally this autolysis mechanism prevents trypsinogen from being activated within the pancreas. However, when the abnormal trypsinogen is activated, it causes a chain reaction where all the trypsinogen in the pancreas is activated, effectively digesting the pancreas from the inside.


==Symptoms and Treatment==
==[[Hereditary pancreatitis historical perspective|Historical Perspective]]==
Symptoms are generally the same as [[acute pancreatitis]], including severe abdominal pain, vomiting, and diarrhea. There is no treatment for the disease, although complications such as malnutrition can be treated with supplimentary pancreatic enzymes.


Most estimates place the number of individuals with hereditary pancreatitis in the United States at 1000.
==[[Hereditary pancreatitis classification|Classification]]==


==References==
==[[Hereditary pancreatitis pathophysiology|Pathophysiology]]==
* {{cite journal |author=Whitcomb D |title=Hereditary pancreatitis: new insights into acute and chronic pancreatitis |journal=Gut |volume=45 |issue=3 |pages=317-22 |year=1999 |pmid=10446089 |url=http://gut.bmjjournals.com/cgi/content/full/45/3/317}}


==[[Hereditary pancreatitis causes|Causes]]==


{{Gastroenterology}}
==[[Hereditary pancreatitis differential diagnosis|Differentiating Xyz  from other Diseases]]==


[[Category:Gastroenterology]]
==[[Hereditary pancreatitis epidemiology and demographics|Epidemiology and Demographics]]==
[[Category:Genetic disorders]]


{{WikiDoc Help Menu}}
==[[Hereditary pancreatitis risk factors|Risk Factors]]==
{{WikiDoc Sources}}
 
'''Bold text'''
==[[Hereditary pancreatitis screening|Screening]]==
 
==[[Hereditary pancreatitis natural history, complications and prognosis|Natural History, Complications and Prognosis]]==
 
==Diagnosis==
[[Hereditary pancreatitis history and symptoms|History and Symptoms]] | [[Hereditary pancreatitis physical examination|Physical Examination]] | [[Hereditary pancreatitis electrocardiogram|Electrocardiogram]] | [[Hereditary pancreatitis laboratory findings|Laboratory Findings]] | [[Hereditary pancreatitis x ray|X-Ray Findings]] | [[Hereditary pancreatitis echocardiography and ultrasound|Echocardiography and Ultrasound]] | [[Hereditary pancreatitis CT scan|CT-Scan Findings]] | [[Hereditary pancreatitis MRI|MRI Findings]] | [[Hereditary pancreatitis other diagnostic studies|Other Diagnostic Studies]] | [[Hereditary pancreatitis other imaging findings|Other Imaging Findings]]
 
==Treatment==
[[Hereditary pancreatitis medical therapy|Medical Therapy]] | [[Hereditary pancreatitis surgery|Surgery]] | [[Hereditary pancreatitis primary prevention|Primary Prevention]] | [[Hereditary pancreatitis secondary prevention|Secondary Prevention]] | [[Hereditary pancreatitis cost-effectiveness of therapy|Cost-Effectiveness of Therapy]] | [[Hereditary pancreatitis future or investigational therapies|Future or Investigational Therapies]]
 
==Case Studies==
[[Hereditary pancreatitis case study one|Case #1]]
 
[[Category: (name of the system)]]

Latest revision as of 16:35, 26 January 2018

Hereditary pancreatitis
Pancreas[1]

Hereditary pancreatitis Microchapters

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Patient Information

Overview

Historical Perspective

Classification

Pathophysiology

Causes

Differentiating Hereditary pancreatitis from other Diseases

Epidemiology and Demographics

Risk Factors

Screening

Natural History, Complications and Prognosis

Diagnosis

Diagnostic Criteria

History and Symptoms

Physical Examination

Laboratory Findings

Electrocardiogram

X-ray

Echocardiography and Ultrasound

CT scan

MRI

Other Imaging Findings

Other Diagnostic Studies

Treatment

Medical Therapy

Surgery

Primary Prevention

Secondary Prevention

Cost-Effectiveness of Therapy

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Guidelines for Management

Case Studies

Case #1

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For patient information, click here

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: : Iqra Qamar M.D.[2]

Synonyms and keywords: Hereditary chronic pancreatitis

Overview

Historical Perspective

Classification

Pathophysiology

Causes

Differentiating Xyz from other Diseases

Epidemiology and Demographics

Risk Factors

Screening

Natural History, Complications and Prognosis

Diagnosis

History and Symptoms | Physical Examination | Electrocardiogram | Laboratory Findings | X-Ray Findings | Echocardiography and Ultrasound | CT-Scan Findings | MRI Findings | Other Diagnostic Studies | Other Imaging Findings

Treatment

Medical Therapy | Surgery | Primary Prevention | Secondary Prevention | Cost-Effectiveness of Therapy | Future or Investigational Therapies

Case Studies

Case #1