Rhabdomyoma classification

Jump to navigation Jump to search

Rhabdomyoma Microchapters

Home

Patient Information

Overview

Historical Perspective

Classification

Pathophysiology

Causes

Differentiating Rhabdomyoma from other Diseases

Epidemiology and Demographics

Risk Factors

Screening

Natural History, Complications and Prognosis

Diagnosis

Staging

History and Symptoms

Physical Examination

Laboratory Findings

Biopsy

Chest X Ray

CT

MRI

Echocardiography or Ultrasound

Other Imaging Findings

Other Diagnostic Studies

Treatment

Medical Therapy

Surgery

Primary Prevention

Secondary Prevention

Cost-Effectiveness of Therapy

Future or Investigational Therapies

Case Studies

Case #1

Rhabdomyoma classification On the Web

Most recent articles

Most cited articles

Review articles

CME Programs

Powerpoint slides

Images

American Roentgen Ray Society Images of Rhabdomyoma classification

All Images
X-rays
Echo & Ultrasound
CT Images
MRI

Ongoing Trials at Clinical Trials.gov

US National Guidelines Clearinghouse

NICE Guidance

FDA on Rhabdomyoma classification

CDC on Rhabdomyoma classification

Rhabdomyoma classification in the news

Blogs on Rhabdomyoma classification

Directions to Hospitals Treating Rhabdomyoma

Risk calculators and risk factors for Rhabdomyoma classification

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]Associate Editor(s)-in-Chief: Simrat Sarai, M.D. [2]

Overview

Enteropathy-associated T-cell Lymphoma (EATL), also enteropathy-type T-cell lymphoma (ETTL), is a type of T-cell non-hodgkin lymphoma that affects the small intestine, it is composed of large lymphoid cells. Enteropathy-associated T-cell lymphoma has two subtypes, type I enteropathy-associated T-cell lymphoma which has a strong association with celiac disease and it is more common in western countries and type II enteropathy-associated T-cell lymphoma which is mostly found among the Asian population. Genes involved in the pathogenesis of this disease include 8q24, T-cell receptor (TCR) beta and gamma, and 16q genes. On gross pathology, multiple intestinal ulcers are characteristic findings of EATL. On microscopic histopathological analysis, monotonous cells, round or angulated vesicular nuclei, and prominent nucleoli are characteristic findings of enteropathy-associated T-cell lymphoma. There are no established causes for enteropathy-associated T-cell lymphoma. EATL must be differentiated from other diseases such as peptic ulcer, poorly-differentiated adenocarcinoma, MALT lymphoma, diffuse large B cell lymphoma, and mantle cell lymphoma.


Classification

Rhabdomyoma may be classified into the following subtypes: [1][2][3][4][5][6]

Neoplastic

Neoplastic rhabdomyomas may be further classified into the following types:

Hamartomataous

Hamartamatous rhabdomyomas may be further classified into the following types:

References

  1. McKinnon EL, Rand AJ, Selim MA, Fuchs HE, Buckley AF, Cummings TJ (October 2015). "Rhabdomyomatous mesenchymal hamartoma presenting as a sacral skin tag in two neonates with spinal dysraphism". J. Cutan. Pathol. 42 (10): 774–8. doi:10.1111/cup.12538. PMID 25989364.
  2. Beghetti M, Gow RM, Haney I, Mawson J, Williams WG, Freedom RM (1997). "Pediatric primary benign cardiac tumors: a 15-year review". Am Heart J. 134 (6): 1107–14. PMID 9424072.
  3. Becker AE (2000). "Primary heart tumors in the pediatric age group: a review of salient pathologic features relevant for clinicians". Pediatr Cardiol. 21 (4): 317–23. doi:10.1007/s002460010071. PMID 10865004.
  4. Elderkin RA, Radford DJ (2002). "Primary cardiac tumours in a paediatric population". J Paediatr Child Health. 38 (2): 173–7. PMID 12031001.
  5. Kocabaş A, Ekici F, Cetin Iİ, Emir S, Demir HA, Arı ME; et al. (2013). "Cardiac rhabdomyomas associated with tuberous sclerosis complex in 11 children: presentation to outcome". Pediatr Hematol Oncol. 30 (2): 71–9. doi:10.3109/08880018.2012.734896. PMID 23151153.
  6. Lu DY, Chang S, Cook H, Alizadeh Y, Karam AK, Moatamed NA, Dry SM (April 2012). "Genital rhabdomyoma of the urethra in an infant girl". Hum. Pathol. 43 (4): 597–600. doi:10.1016/j.humpath.2011.06.012. PMID 21992817.
  7. White LR, Agrawal V, Sutton L, Balbosa AC (June 2015). "Rhabdomyomatous mesenchymal hamartoma of the face causing trigeminal neuralgia". Am J Case Rep. 16: 338–40. doi:10.12659/AJCR.893719. PMC 4460909. PMID 26037964.

Template:WH Template:WS