Cystic fibrosis chest x ray: Difference between revisions

Jump to navigation Jump to search
 
(24 intermediate revisions by 2 users not shown)
Line 4: Line 4:
{{CMG}}; {{AE}} {{SHH}}
{{CMG}}; {{AE}} {{SHH}}
==Overview==
==Overview==
In cystic fibrosis the [[Chest X-ray|chest radiographic]] features may overlap with many other disorders, particularly those characterized by [[Inflammation|inflammatory]] or destructive changes of the [[Airway|airways]]. [[Atelectasis]] is common in [[Infant|infancy]]. Most patients with CF demonstrate some of the classic [[Chest X-ray|chest radiographic]] findings that reflect chronic [[bronchiectasis]], including hyperinflation, [[Peribronchial cuffing|peribronchial thickening]] and [[Dilation|dilatation]], [[peribronchial cuffing]], [[Mucoid plaque|mucoid impaction]], [[Cyst|cystic]] radiolucencies, increase in [[interstitial]] marking, and scattered [[Nodule (medicine)|nodular]] densities.


==X Ray==
==X Ray==
* In cystic fibrosis chest radiographs may be normal early in life.
* In cystic fibrosis [[Chest X-ray|chest radiographs]] may be normal early in life.
* The [[Chest X-ray|chest radiographic]] features may overlap with many other disorders, particularly those characterized by [[Inflammation|inflammatory]] or destructive changes of the [[Airway|airways]].
* Hyperinflation due to [[Mucoid plaque|mucus plugging]] of small [[Bronchiole|bronchioles]] is the earliest [[Radiography|radiographic]] sign of cystic fibrosis in [[Infant|infants]] and children.
* [[Atelectasis]] (especially in right upper lobe) is common in [[Infant|infancy]].<ref name="pmid24605255">{{cite journal |vauthors=Odev K, Guler I, Altinok T, Pekcan S, Batur A, Ozbiner H |title=Cystic and cavitary lung lesions in children: radiologic findings with pathologic correlation |journal=J Clin Imaging Sci |volume=3 |issue= |pages=60 |date=2013 |pmid=24605255 |pmc=3935260 |doi=10.4103/2156-7514.124087 |url=}}</ref>


* Findings on an chest x ray suggestive of cystic fibrosis include:<ref name="pmid24605255">{{cite journal |vauthors=Odev K, Guler I, Altinok T, Pekcan S, Batur A, Ozbiner H |title=Cystic and cavitary lung lesions in children: radiologic findings with pathologic correlation |journal=J Clin Imaging Sci |volume=3 |issue= |pages=60 |date=2013 |pmid=24605255 |pmc=3935260 |doi=10.4103/2156-7514.124087 |url=}}</ref>
*Most patients with CF demonstrate some of the classic [[Chest X-ray|chest radiographic]] findings that reflect [[Chronic (medical)|chronic]] [[bronchiectasis]]:<ref name="pmid1475543">{{cite journal |vauthors=Grum CM, Lynch JP |title=Chest radiographic findings in cystic fibrosis |journal=Semin Respir Infect |volume=7 |issue=3 |pages=193–209 |date=September 1992 |pmid=1475543 |doi= |url=}}</ref><ref name="pmid24065629">{{cite journal |vauthors=Vult von Steyern K, Björkman-Burtscher IM, Geijer M |title=Radiography, tomosynthesis, CT and MRI in the evaluation of pulmonary cystic fibrosis: an untangling review of the multitude of scoring systems |journal=Insights Imaging |volume=4 |issue=6 |pages=787–98 |date=December 2013 |pmid=24065629 |pmc=3846934 |doi=10.1007/s13244-013-0288-y |url=}}</ref>
**The chest radiographic features overlap with many other disorders, particularly those characterized by inflammatory or destructive changes of the airways.
**Hyperinflation
**Hyperinflation due to mucus plugging of small bronchioles is the earlist radiographic sign of cystic fibrosis in infants and children.
**[[Bronchiole|Bronchial]] thickening and [[Dilation|dilatation]]
**Atelectasis (especially in right upper lobe) is common in infancy.
**[[Peribronchial cuffing]]
**[[Mucoid plaque|Mucoid]] impaction
**[[Cyst|Cystic]] radiolucencies
**Increase in [[interstitial]] markings
**Scattered [[Nodule (medicine)|nodular]] densities
*Abdominal [[X-rays|x ray]] may show dilated loops of bowel.
 
{|
|
[[File:Meconium-ileus-neonate-with-cystic-fibrosis.jpg|thumb|200px|left|Dilated loops of bowel Source:Case courtesy of Dr Michael Sargent, Radiopaedia.org, rID: 6009<ref name="urlCystic fibrosis | Radiology Case | Radiopaedia.org">{{cite web |url=https://radiopaedia.org/cases/cystic-fibrosis-2 |title=Cystic fibrosis &#124; Radiology Case &#124; Radiopaedia.org |format= |work= |accessdate=}}</ref>]]
|
[[File:Cystic-fibrosis-2.jpeg|thumb|200px|left|Advanced bronchiectasis: ring shadows and tram-track opacities are seen throughout both lungs, particularly well in the uppers zone Source: Case courtesy of A.Prof Frank Gaillard, Radiopaedia.org, rID: 8247<ref name="urlCystic fibrosis | Radiology Case | Radiopaedia.org">{{cite web |url=https://radiopaedia.org/cases/cystic-fibrosis-2 |title=Cystic fibrosis &#124; Radiology Case &#124; Radiopaedia.org |format= |work= |accessdate=}}</ref>]]
|}


==References==
==References==
Line 17: Line 33:


{{WH}}
{{WH}}
{{WS}}
 
[[Category: (name of the system)]]
[[Category:Medicine]]
[[Category:Up-To-Date]]
[[Category:Gastroenterology]]
[[Category:Pediatrics]]
[[Category:Pulmonology]]

Latest revision as of 20:44, 29 March 2018

Cystic fibrosis Microchapters

Home

Patient Information

Overview

Historical Perspective

Classification

Pathophysiology

Causes

Differentiating Cystic fibrosis from other Diseases

Epidemiology and Demographics

Risk Factors

Screening

Natural History, Complications and Prognosis

Diagnosis

Diagnostic Study of Choice

History and Symptoms

Physical Examination

Laboratory Findings

Electrocardiogram

Chest X Ray

Echocardiography or Ultrasound

CT

MRI

Other Imaging Findings

Other Diagnostic Studies

Treatment

Medical Therapy

Surgery

Primary Prevention

Secondary Prevention

Cost-Effectiveness of Therapy

Future or Investigational Therapies

Case Studies

Case #1

Cystic fibrosis chest x ray On the Web

Most recent articles

cited articles

Review articles

CME Programs

Powerpoint slides

Images

American Roentgen Ray Society Images of Cystic fibrosis chest x ray

All Images
X-rays
Echo & Ultrasound
CT Images
MRI

Ongoing Trials at Clinical Trials.gov

US National Guidelines Clearinghouse

NICE Guidance

FDA on Cystic fibrosis chest x ray

CDC on Cystic fibrosis chest x ray

Cystic fibrosis chest x ray in the news

Blogs on Cystic fibrosis chest x ray

Directions to Hospitals Treating Cystic fibrosis

Risk calculators and risk factors for Cystic fibrosis chest x ray

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Shaghayegh Habibi, M.D.[2]

Overview

In cystic fibrosis the chest radiographic features may overlap with many other disorders, particularly those characterized by inflammatory or destructive changes of the airways. Atelectasis is common in infancy. Most patients with CF demonstrate some of the classic chest radiographic findings that reflect chronic bronchiectasis, including hyperinflation, peribronchial thickening and dilatation, peribronchial cuffing, mucoid impaction, cystic radiolucencies, increase in interstitial marking, and scattered nodular densities.

X Ray

Dilated loops of bowel Source:Case courtesy of Dr Michael Sargent, Radiopaedia.org, rID: 6009[4]
Advanced bronchiectasis: ring shadows and tram-track opacities are seen throughout both lungs, particularly well in the uppers zone Source: Case courtesy of A.Prof Frank Gaillard, Radiopaedia.org, rID: 8247[4]

References

  1. Odev K, Guler I, Altinok T, Pekcan S, Batur A, Ozbiner H (2013). "Cystic and cavitary lung lesions in children: radiologic findings with pathologic correlation". J Clin Imaging Sci. 3: 60. doi:10.4103/2156-7514.124087. PMC 3935260. PMID 24605255.
  2. Grum CM, Lynch JP (September 1992). "Chest radiographic findings in cystic fibrosis". Semin Respir Infect. 7 (3): 193–209. PMID 1475543.
  3. Vult von Steyern K, Björkman-Burtscher IM, Geijer M (December 2013). "Radiography, tomosynthesis, CT and MRI in the evaluation of pulmonary cystic fibrosis: an untangling review of the multitude of scoring systems". Insights Imaging. 4 (6): 787–98. doi:10.1007/s13244-013-0288-y. PMC 3846934. PMID 24065629.
  4. 4.0 4.1 "Cystic fibrosis | Radiology Case | Radiopaedia.org".

Template:WH