Sandbox:Sahar

Lipomatous tumor	Age of onset	Clinical features	Diagnostic feature(s)	Other features
Angiomyolipoma
	Infancy, but may be delayed until adulthood	Non-pruritic urticarial rash Fever Headache Fatigue Conjunctivitis	Ice cube test is negative	Cold-induced rash Skin biopsy shows increased neutrophils at the eccrine coils
Schnitzler Syndrome	Middle age	Chronic urticarial rash Fever Arthralgia Bone pain	Monoclonal gammopathy	Rash is the presenting sign Neutrophillic infiltrate in dermis Dermographism
Deficiency in Interleukin-1 Receptor Antagonist	Infancy	Pustular rash Bone pain Swollen joints Aphthous ulcers	Occurs due to mutation in IL1RN gene Pustular rash similar to pustular psoriasis	Epidermal neutrophilic pustules at hair follicles Pathergy Hyperkeratosis and acanthosis High neutrophil infiltrate of the dermis
Systemic-Onset Juvenile Idiopathic Arthritis	2-16 years of age	High fever Arthralgia Generalized lymphadenopathy Splenomegaly	Evanescent rash Bright salmon-pink Morbilliform, macular rash Rash presents with onset of fever	May cause amyloidosis
Adult-Onset Still’s Disease	16-35 years May affect all ages	High spiking fever Joint pain Skin rash Lymphadenopathy Splenomegaly	Evanescent salmon-colored bumpy rash Pruritic rash on the proximal limbs and trunk	More commonly seen among women May cause destructive arthritis

Example #1

The patient presented with S.O.B. one year after hysterectomy for a leiomyomatous uterus.

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  CT in Intravenous leiomyomatosis

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