Tricuspid atresia differential diagnosis
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor-In-Chief: Keri Shafer, M.D. [2] Priyamvada Singh, MBBS [[3]]; Assistant Editor-In-Chief: Kristin Feeney, B.S. [[4]]
Overview
Differentiating Tricuspid atresia from other Diseases
Patients with tricuspid atresia should be differentiated from other cardiac and non-cardiac causes of cyanosis-
Cardiac causes (starts with 't'):
- Tetralogy of Fallot
- Truncus arteriosus
- Total anomalous pulmonary venous connection
- Other tricuspid valve abnormalities like tricuspid regurgitaton, tricuspid stenosis
Other less common causes are- pulmonary atresia, hypoplastic left heart syndrome, anomalous systemic venous connection.
Non-cardiac causes:
- Pulmonary diseases - Structural abnormalities of the lung, V/P (ventilation-perfusion mismatch), airway obstruction, pneumothorax, and hypoventilation.
- Abnormal hemoglobin like methemoglobin, polycythemia
- Peripheral cyanosis for e.g. sepsis, hypoglycemia, dehydration, and hypoadrenalism.