Noncompaction cardiomyopathy natural history: Difference between revisions
| Line 3: | Line 3: | ||
==Overview== | ==Overview== | ||
The presence of NCC | The presence of NCC is associated with [[congestive heart failure]] and disesae in other organs. | ||
==Complications and Associated Involvement of Other Organs== | |||
===Cardiac Disease=== | |||
* Abnormalities of the origin of the [[left coronary artery]] | |||
* [[Pulmonary atresia]] | |||
* [[Pulmonary stenosis]] | |||
* Right or Left ventricle obstruction | |||
* [[Hypoplastic left heart syndrome|Hypoplastic left ventricle]] | |||
* [[Mitral regurgitation]] | |||
* [[Tachyarrhythmias]] and [[sudden cardiac death]] | |||
* Thrombus formation in the [[left ventricle]] | |||
===Neurologic Complications=== | |||
* [[Becker's muscular dystrophy]] | |||
* [[Mitochondrial myopathy]] | |||
* [[Myopathy|Polyneuropathy and metabolic myopathy]] | |||
===Associated Genetic Disorders=== | |||
* [[Emery-Dreifuss muscular dystrophy]] | |||
* [[Muscular dystrophy|Myotubular cardiomyopathy]] | |||
* [[Barth syndrome]] | |||
==Prognosis== | ==Prognosis== | ||
Revision as of 02:43, 3 August 2011
|
Noncompaction Cardiomyopathy Microchapters |
|
Pathophysiology |
|---|
|
Differentiating Noncompaction Cardiomyopathy from other Diseases |
|
Diagnosis |
|
Treatment |
|
Noncompaction cardiomyopathy natural history On the Web |
|
Risk calculators and risk factors for Noncompaction cardiomyopathy natural history |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Overview
The presence of NCC is associated with congestive heart failure and disesae in other organs.
Complications and Associated Involvement of Other Organs
Cardiac Disease
- Abnormalities of the origin of the left coronary artery
- Pulmonary atresia
- Pulmonary stenosis
- Right or Left ventricle obstruction
- Hypoplastic left ventricle
- Mitral regurgitation
- Tachyarrhythmias and sudden cardiac death
- Thrombus formation in the left ventricle
Neurologic Complications
Associated Genetic Disorders
Prognosis
In so far as noncompaction cardiomyopathy is a recently described entity, its association with long term clinical outcomes is not known. In a 2005 study [1] which documented the long term follow up of 34 patients who were symptomatic with NCC, 35% had died at the age of 42 +/- 40 months. 12% of the patients required cardiac transplantation due to heart failure. However, this study was based upon symptomatic patients referred to a tertiary care center, and so were suffering from more severe forms of NCC than might be found typically in the population. As NCC is a genetic disease, as a precaution immediate family members are being tested which is turning up more supposedly healthy people with NCC who are not suffering from it. The long term prognosis for these people is currently unknown.
References
- ↑ Oechslin, Erwin; Jenni, Rolf (2005). "Non-compaction of the Left Ventricular Myocardium - From Clinical Observation to the Discovery of a New Disease" (webpage).