Pulmonary atresia: Difference between revisions
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- The reported incidence is 6-8 per 100,000 live births and 1-3% of all congenital heart disease. [https://www.uptodate.com/contents/pulmonary-atresia-with-intact-ventricular-septum-pa-ivs?search=pulmonary%20atresia&source=search_result&selectedTitle=1~150&usage_type=default&display_rank=1#H172915282][https://emedicine.medscape.com/article/898167-overview#a6] | - The reported incidence is 6-8 per 100,000 live births and 1-3% of all congenital heart disease. [https://www.uptodate.com/contents/pulmonary-atresia-with-intact-ventricular-septum-pa-ivs?search=pulmonary%20atresia&source=search_result&selectedTitle=1~150&usage_type=default&display_rank=1#H172915282][https://emedicine.medscape.com/article/898167-overview#a6] | ||
==[[Pulmonary atresia classifications|Classification]]== | ==[[Pulmonary atresia classifications|Classification]]== | ||
Revision as of 02:21, 18 June 2020
For patient information click here
| Pulmonary atresia | ||
| ICD-10 | Q25.5 | |
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| ICD-9 | 747.3 | |
| MedlinePlus | 001091 | |
| MeSH | C14.240.670 | |
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Pulmonary atresia Microchapters |
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Diagnosis |
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Treatment |
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Pulmonary atresia On the Web |
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American Roentgen Ray Society Images of Pulmonary atresia |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-In-Chief: Muhammad Waqas
Overview
Pathophysiology
Epidemiology and demographics
- While there is no difference in the incidence of Pulmonary atresia in male or female, it is found that pulmonary atresia with VSD ( PA-VSD ) is slightly more prevalent in males than in females. [2][3]
1) The prevalence of Pulmonary Atresia with VSD is estimated to be around 0.07 per 1000 live breath. and 2.5-3.4 % among all congenital heart diseases.[4]
2) The overall incidence of PA-IVSD is under estimated as most of the fetus are spontaneously aborted due to the underlying other congenital malformations or are diagnosed on routine antenatal ultrasound and results in elective termination.
- The reported incidence is 6-8 per 100,000 live births and 1-3% of all congenital heart disease. [5][6]
Classification
Natural history, Complications, and Prognosis
Causes
Differentiating Pulmonary atresia from other Disorders
As Pulmonic valva atresia presents with the signs and symptoms of right ventricular outflow obstruction, it can be confused with the disease with similar presentation. Diagnosis can be made on the basis of Echocardiographic findings. Conditions sharing the pulmonic outflow obstructions are;
1) Tetralogy of Fallot
2) Critical Pulmonary Stenosis
3) Tricuspid Atresia
Diagnosis
History and Symptoms | Physical Examination | Laboratory Tests | Electrocardiogram | Chest X Ray | MRI | CT | Echocardiography | Other Imaging Findings | Other Diagnostic Studies
Treatment
Medical: Medical Therapy
Surgical: Surgery
Primary Prevention | Secondary Prevention | Cost-Effectiveness of Therapy | Future or Investigational Therapies