| Porphyrin biosynthesis | initial mitochondrial: Aminolevulinic acid synthase - Porphobilinogen synthase
cytosolic: Porphobilinogen deaminase - Uroporphyrinogen III synthase - Uroporphyrinogen III decarboxylase - Coproporphyrinogen III oxidase terminal mitochondrial: Protoporphyrinogen oxidase - Ferrochelatase |
|---|---|
| Heme breakdown to bile | |
see also disorders, intermediates | |