Primary ciliary dyskinesia electrocardiogram

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Primary ciliary dyskinesia Microchapters

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor(s)-in-Chief: Hafsa Ghaffar, M.B.B.S[2]

Overview

Primary ciliary dyskinesia occasionally presents with dextrocardia and situs inversus totalis, non functioning cilia in the embryonal node could be responsible for this mal positioning. Ecg shows right axis deviation, a finding if present should warrant further testing.

Electrocardiogram

Primary ciliary dyskinesia is occasionally associated with situs inversus totalis and dextrocardia. Ecg could detect dextrocardia and warrant for additional testing in individuals. Ecg demonstrates the following changes:

References

  1. "Dextrocardia • LITFL • ECG Library Diagnosis".

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