Erdheim-Chester disease overview

Erdheim-Chester disease Microchapters
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Overview

Erdheim-Chester disease is a rare form of non-Langerhans-cell histiocytosis. Usually, onset is in middle age. The disease involves an infiltration of lipid-laden macrophages, multinucleated giant cells, an inflammatory infiltrate of lymphocytes and histiocytes in the bone marrow, and a generalized sclerosis of the long bones.