Congenital cystic adenomatoid malformation

Jump to: navigation, search

WikiDoc Resources for Congenital cystic adenomatoid malformation

Articles

Most recent articles on Congenital cystic adenomatoid malformation

Most cited articles on Congenital cystic adenomatoid malformation

Review articles on Congenital cystic adenomatoid malformation

Articles on Congenital cystic adenomatoid malformation in N Eng J Med, Lancet, BMJ

Media

Powerpoint slides on Congenital cystic adenomatoid malformation

Images of Congenital cystic adenomatoid malformation

Photos of Congenital cystic adenomatoid malformation

Podcasts & MP3s on Congenital cystic adenomatoid malformation

Videos on Congenital cystic adenomatoid malformation

Evidence Based Medicine

Cochrane Collaboration on Congenital cystic adenomatoid malformation

Bandolier on Congenital cystic adenomatoid malformation

TRIP on Congenital cystic adenomatoid malformation

Clinical Trials

Ongoing Trials on Congenital cystic adenomatoid malformation at Clinical Trials.gov

Trial results on Congenital cystic adenomatoid malformation

Clinical Trials on Congenital cystic adenomatoid malformation at Google

Guidelines / Policies / Govt

US National Guidelines Clearinghouse on Congenital cystic adenomatoid malformation

NICE Guidance on Congenital cystic adenomatoid malformation

NHS PRODIGY Guidance

FDA on Congenital cystic adenomatoid malformation

CDC on Congenital cystic adenomatoid malformation

Books

Books on Congenital cystic adenomatoid malformation

News

Congenital cystic adenomatoid malformation in the news

Be alerted to news on Congenital cystic adenomatoid malformation

News trends on Congenital cystic adenomatoid malformation

Commentary

Blogs on Congenital cystic adenomatoid malformation

Definitions

Definitions of Congenital cystic adenomatoid malformation

Patient Resources / Community

Patient resources on Congenital cystic adenomatoid malformation

Discussion groups on Congenital cystic adenomatoid malformation

Patient Handouts on Congenital cystic adenomatoid malformation

Directions to Hospitals Treating Congenital cystic adenomatoid malformation

Risk calculators and risk factors for Congenital cystic adenomatoid malformation

Healthcare Provider Resources

Symptoms of Congenital cystic adenomatoid malformation

Causes & Risk Factors for Congenital cystic adenomatoid malformation

Diagnostic studies for Congenital cystic adenomatoid malformation

Treatment of Congenital cystic adenomatoid malformation

Continuing Medical Education (CME)

CME Programs on Congenital cystic adenomatoid malformation

International

Congenital cystic adenomatoid malformation en Espanol

Congenital cystic adenomatoid malformation en Francais

Business

Congenital cystic adenomatoid malformation in the Marketplace

Patents on Congenital cystic adenomatoid malformation

Experimental / Informatics

List of terms related to Congenital cystic adenomatoid malformation

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Overview

Congenital cystic adenomatoid malformation (CCAM) is a congenital disorder similar to bronchopulmonary sequestration. In CCAM, usually an entire lobe of lung is replaced by a non-working cystic piece of abnormal lung tissue. This abnormal tissue will never function as normal lung tissue.

In most cases the outcome of a fetus with CCAM is very good. However in a rare few cases the cystic mass grows so large as to limit the growth of the surrounding lung and cause pressure against the heart. In these situations, the CCAM can be life-threatening for the fetus.

Diagnosis

CCAMs are often identified during routine prenatal ultrasonography. Indentifying characteristics on the sonogram include: an echogenic (bright) mass appearing in the chest of the fetus, displacement of the heart from its normal position, a flat or everted (pushed downward) diaphragm, or the absence of visible lung tissue.

CCAMS are classified into three different types based largely on their gross appearance. Type I has large (>2 cm) multiloculated cysts. Type II has smaller uniform cysts. Type III is not grossly cystic, referred to as the "adenomatoid" type. Microscopically, the lesions are not true cysts, but communicate with the surrounding parenchyma.

Treatment

In most cases, a fetus with CCAM is closely monitored during pregnancy and the CCAM is removed via surgery after birth. A few fetuses may develop fluid collections within the chest cavity and in those situations a Harrision catheter shunt can be used to drain the fluid into the amniotic fluid.

Very large cystic masses might pose dangerous during birth because of the airway compression. In this situation, a special surgical type of delivery called the EXIT procedure may be used.

In rare extreme cases, where fetus's heart is in danger, fetal surgery can be performed to remove the CCAM. If non-immune hydrops fetalis develop, there is a near universal mortality of the fetus. Fetal surgery can improve the survival percentage up to 50-60%.



Linked-in.jpg