Arrhythmogenic right ventricular dysplasia epidemiology and demographics

Jump to navigation Jump to search

Arrhythmogenic right ventricular dysplasia Microchapters

Home

Overview

Historical Perspective

Classification

Pathophysiology

Causes

Differentiating Arrhythmogenic right ventricular dysplasia from other Diseases

Epidemiology and Demographics

Risk Factors

Screening

Natural History, Complications and Prognosis

Diagnosis

Diagnostic Criteria

History and Symptoms

Physical Examination

Laboratory Findings

X - Ray

ECG

Cardiac MRI

Echocardiogram

Other Imaging Findings

Endomyocardial biopsy

Atuopsy

Treatment

Medical Therapy

Surgery

Primary Prevention

Secondary Prevention

Future or Investigational Therapies

Arrhythmogenic right ventricular dysplasia epidemiology and demographics On the Web

Most recent articles

Most cited articles

Review articles

CME Programs

Powerpoint slides

Images

American Roentgen Ray Society Images of Arrhythmogenic right ventricular dysplasia epidemiology and demographics

All Images
X-rays
Echo & Ultrasound
CT Images
MRI

Ongoing Trials at Clinical Trials.gov

National Guidelines Clearinghouse

NICE Guidance

FDA on Arrhythmogenic right ventricular dysplasia epidemiology and demographics

CDC on Arrhythmogenic right ventricular dysplasia epidemiology and demographics

Arrhythmogenic right ventricular dysplasia epidemiology and demographics in the news

Blogs onArrhythmogenic right ventricular dysplasia epidemiology and demographics

Directions to Hospitals Treating Arrhythmogenic right ventricular dysplasia

Risk calculators and risk factors for Arrhythmogenic right ventricular dysplasia epidemiology and demographics

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Overview

ARVD is a rare disease. It is observed more commonly in males, and accounts for 17% of all sudden cardiac deaths in the young.

Epidemiology and demographics

Incidence

The incidence of ARVC/D is difficult to be determined due the different clinical manifestations of the disease which vary greatly, especially in different ethnic groups. This could be secondary to the genetic heterogeneity and variable phenotype expression, diverse disease progression. All this make the diagnosis difficult and decreases the real evaluation of the incidence.

  • The incidence of ARVD is about 1/10,000 in the general population in the United States, although some studies have suggested that it may be as common as 1/1,000.
  • In Italy, the incidence is 40/10,000, making it the most common cause of sudden cardiac death in the young population. It is more common in Northern Italy [1][2]

Prevalence

  • The estimated prevalence of ARVC/D in the general population is approximately 1:5000
  • ARVC/D accounts for 11%–22% of cases of SCD in the young athlete patient population[3][4]
  • It accounts for approximately 22% of cases in athletes in northern Italy and about 17% of SCD in young people in the United States

Gender

  • Men are more frequently affected than women, with a male to female ratio of 3:1

References

  1. Lahtinen AM, Lehtonen E, Marjamaa A, Kaartinen M, Heliö T, Porthan K; et al. (2011). "Population-prevalent desmosomal mutations predisposing to arrhythmogenic right ventricular cardiomyopathy". Heart Rhythm. 8 (8): 1214–21. doi:10.1016/j.hrthm.2011.03.015. PMID 21397041.
  2. Peters S, Trümmel M, Meyners W (2004). "Prevalence of right ventricular dysplasia-cardiomyopathy in a non-referral hospital". Int J Cardiol. 97 (3): 499–501. doi:10.1016/j.ijcard.2003.10.037. PMID 15561339.
  3. Thiene G, Nava A, Corrado D, Rossi L, Pennelli N (1988). "Right ventricular cardiomyopathy and sudden death in young people". N Engl J Med. 318 (3): 129–33. doi:10.1056/NEJM198801213180301. PMID 3336399.
  4. Corrado D, Basso C, Schiavon M, Thiene G (1998). "Screening for hypertrophic cardiomyopathy in young athletes". N Engl J Med. 339 (6): 364–9. doi:10.1056/NEJM199808063390602. PMID 9691102.

Template:WH Template:WS