Takayasu's arteritis classification

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor(s)-in-Chief: Farnaz Khalighinejad, MD [2]

Overview

Takayasu arteritis may be classified according to angiographic findings into 6 types which is useful in planning for surgery. The most commonly involved vessels include the left subclavian artery (50%), left common carotid artery (20%), brachiocephalic trunk, renal arteries, celiac trunksuperior mesenteric artery, and pulmonary arteries (50%). Takayasu arteritis may be classified according to clinical finding into 4 groups of group I, IIA, IIB, and III.

Classification

  • Takayasu arteritis may be classified according to angiographic findings into 6 types:[1]
Type Vessel involvement
Type I Branches from the aortic arch
Type IIa Ascending aorta, aortic arch and its branches
Type IIb Ascending aorta, aortic arch and its branches, thoracic descending aorta
Type III Thoracic descending aorta, abdominal aorta, and/or renal arteries
Type IV Abdominal aorta and/or renal arteries
Type V Combined features of types IIb and IV
  • Takayasu arteritis may be classified according to clinical finding into 4 groups:[2]
Group Clinical features
Group I Uncomplicated disease, with or without pulmonary artery involvement
Group IIA Mild/moderate single complication together with uncomplicated disease
Group IIB Severe single complication together with uncomplicated disease
Group III Two or more complications together with uncomplicated disease

References

  1. Moriwaki R, Noda M, Yajima M, Sharma BK, Numano F (May 1997). "Clinical manifestations of Takayasu arteritis in India and Japan--new classification of angiographic findings". Angiology. 48 (5): 369–79. doi:10.1177/000331979704800501. PMID 9158381.
  2. Ishikawa K (January 1978). "Natural history and classification of occlusive thromboaortopathy (Takayasu's disease)". Circulation. 57 (1): 27–35. PMID 21760.