Right ventricular outflow tract obstruction pulmonary subvalvular stenosis: Difference between revisions

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(New page: {{SI}} {{CMG}} '''Associate Editor-In-Chief:''' {{CZ}} '''Associate Editor-in-Chief:''' Keri Shafer, M.D. [mailto:kshafer@bidmc.harvard.edu] {{EH}} == Anatomy == ...)
 
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'''Associate Editor-in-Chief:''' [[User:KeriShafer|Keri Shafer, M.D.]] [mailto:kshafer@bidmc.harvard.edu]
'''Associate Editor-in-Chief:''' [[User:KeriShafer|Keri Shafer, M.D.]] [mailto:kshafer@bidmc.harvard.edu]


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== Anatomy ==
== Anatomy ==

Revision as of 15:45, 20 August 2012

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Associate Editor-In-Chief: Cafer Zorkun, M.D., Ph.D. [2]

Associate Editor-in-Chief: Keri Shafer, M.D. [3]


Anatomy

  • There is hypertrophy of the infundibular muscle causing obstruction.
  • The isolated form is rare, more commonly develops in response to an underlying VSD.

Clinical Features

  • Similar to valvar pulmonic stenosis.
  • No ejection click in contrast to valvar pulmonic stenosis.
  • No poststenotic dilation of the pulmonary artery in contrast to valvar pulmonic stenosis.

References

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