Pityriasis lichenoides et varioliformis acuta

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Pityriasis lichenoides et varioliformis acuta

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Kiran Singh, M.D. [2]

Synonyms and keywords:

Overview

Pityriasis Lichenoides et Varioliformis Acuta, or Mucha Habermann's Disease, short form PLEVA, is a disease of the immune system. It is the more severe version of Pityriasis lichenoides chronica. The disease is characterized by rashes and small lesions on the skin. The disease is most common in males and usually occurs in childhood, although it has been seen in every age group and every race. It is possible for the disease to go into remission for short periods of time or forever.

Historical Perspective

Classification

Pathophysiology

Causes

Differentiating Pityriasis Lichenoides et Varoliformis Acuta from other Diseases

  • It is commonly misdiagnosed as chickenpox or rosacea.

Epidemiology and Demographics

Age

Gender

Race

Risk Factors

Natural History, Complications and Prognosis

  • Prognosis is usually good with treatment.

Diagnosis

Diagnostic criteria

The most common way to diagnose is by biopsy.

History and Symptoms

Physical Examination

Skin

Trunk

Laboratory Findings

Imaging Findings

Other Diagnostic Studies

Treatment

Medical therapy

It is not contagious and currently there is no cure for the disease, although the lesions can be treated with ultraviolet therapy as well as topical steroids and antibiotics.

Treatment often involves multiple therapies that address the immune system and bacterial, viral, or dermatological causes.

Surgery

Prevention

See also

External links

References

  1. 1.00 1.01 1.02 1.03 1.04 1.05 1.06 1.07 1.08 1.09 1.10 1.11 1.12 1.13 1.14 1.15 1.16 1.17 1.18 1.19 1.20 1.21 1.22 1.23 1.24 1.25 1.26 1.27 "Dermatology Atlas".

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