Lymphangiomyomatosis: Difference between revisions

Jump to navigation Jump to search
No edit summary
Line 6: Line 6:


==Overview==
==Overview==
Lymphangiomyocytosis is defined as a multifocal neoplasm with differentiation of the perivascular epithelioid cell and has a female prepondrance, especially females of child-bearing age.  
Lymphangiomyocytosis is defined as a multifocal neoplasm with differentiation of the perivascular epithelioid cell and has a female prepondrance, especially females of child-bearing age.


==Characteristic Features==
==Characteristic Features==

Revision as of 17:47, 14 September 2012

Template:Lymphangiomyomatosis Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-In-Chief: Varun Kumar, M.B.B.S. [2]

Synonyms and keywords: Lymphangioleiomyomatosis; LAM

Overview

Lymphangiomyocytosis is defined as a multifocal neoplasm with differentiation of the perivascular epithelioid cell and has a female prepondrance, especially females of child-bearing age.

Characteristic Features

Lymphangiomyocytosis is characterized by the presence of smooth muscle and epithelioid cells and by the proliferation of lymphatic vessels.

Sites of Involvement

  • Lungs,
  • Mediastinum, and
  • Retroperitoneum.

Presentation

It usually presents with chylous pleural effusion or ascites.

Diagnosis

Chest X-ray

Reference

Template:WH Template:WS