Long QT syndrome Moss and Schwartz Score

ECG

QTc

<480 msec 3

460–470 msec 2

450 msec (males) 1

• Torsades de pointes 2
• T-wave alternans 1
• Notched T wave in 3 leads 1
• Low heart rate for age 0.5

Clinical History

Syncope

• With stress 2
• Without stress 1
• Congenital deafness 0.5

Family History

• Family member with long QT syndrome 1
• Sudden death in a family member >30 years of age with no other identifiable cause 0.5

Cumulative point score for risk of having congential long QT syndrome: 1 = low risk 2–3 = intermediate risk 4 = high risk