Hereditary spherocytosis secondary prevention: Difference between revisions

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{{Hereditary spherocytosis}}
{{Hereditary spherocytosis}}
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==Overview==
==Overview==
The administration of [[Vaccine|vaccines]] including [[Pneumococcal vaccine|pneumococcal]], [[Haemophilus influenzae|hemophilus influenzae]], [[Neisseria meningitidis|meningococcal]] and [[Influenza vaccine|influenza]] should be given two to three weeks before [[splenectomy]]. [[Folic Acid|Folic acid]] supplementation as well as oral [[penicillin]] is also suggested for postsplenectomy [[Patient|patients]] untill reaching [[Adult|adulthood]].


==Secondary Prevention==
==Secondary Prevention==
* In general, once the diagnosis and baseline severity of HS in a child are established, it is not necessary to perform repeated blood tests unless there is an additional clinical indication (such as intercurrent infection and pallor, or an increase in jaundice). A routine annual review is usually sufficient together with an open door policy for potential complications such as parvovirus infection, or abdominal pain, which may trigger investigation for gallstones.
* The administration of [[Vaccine|vaccines]] ([[Pneumococcal vaccine|pneumococcal]], [[haemophilus influenzae type b]], [[Neisseria meningitidis|meningococcal group C]] and [[Influenza vaccine|influenza]]) is indicated 2 to 3 weeks before [[splenectomy]].<ref>{{Cite journal
| author = [[Sayeeda Huq]], [[Mark A. C. Pietroni]], [[Hafizur Rahman]] & [[Mohammad Tariqul Alam]]
| title = Hereditary spherocytosis
| journal = [[Journal of health, population, and nutrition]]
| volume = 28
| issue = 1
| pages = 107–109
| year = 2010
| month = February
| pmid = 20214092
}}</ref>
* Postsplenectomy [[Patient|patients]] should also be given 1mg of [[Folic Acid|folic acid]] daily for preventing secondary [[folic acid deficiency]] and oral [[penicillin]] ([[penicillin V]]) for preventing [[secondary infection]] until reaching [[Adult|adulthood]].
* In general, once the [[diagnosis]] and baseline severity of [[hereditary spherocytosis]] in a [[child]] are established, it is not necessary to perform repeated [[Blood test|blood tests]] unless there is an additional [[clinical]] [[Indication (medicine)|indication]] (such as intercurrent [[infection]] and [[pallor]], or an increase in [[jaundice]]).<ref>{{cite web |url=http://dx.doi.org/10.1136/adc.2003.034587 |title=Hereditary spherocytosis; new guidelines &#124; Archives of Disease in Childhood |format= |work= |accessdate=}}</ref>
* Avoidance of precipitants of hemolysis (such as sulfa drugs or quinines) and certain foods (such as fava beans) may help prevent hemolysis.


==References==
==References==

Latest revision as of 04:03, 19 December 2018

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Shyam Patel [2] Associate Editor(s)-in-Chief:

Overview

The administration of vaccines including pneumococcal, hemophilus influenzae, meningococcal and influenza should be given two to three weeks before splenectomy. Folic acid supplementation as well as oral penicillin is also suggested for postsplenectomy patients untill reaching adulthood.

Secondary Prevention

References

  1. Sayeeda Huq, Mark A. C. Pietroni, Hafizur Rahman & Mohammad Tariqul Alam (2010). "Hereditary spherocytosis". Journal of health, population, and nutrition. 28 (1): 107–109. PMID 20214092. Unknown parameter |month= ignored (help)
  2. "Hereditary spherocytosis; new guidelines | Archives of Disease in Childhood".

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