Henoch-Schönlein purpura (patient information)

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Henoch-Schönlein purpura
ICD-10 D69.0
(ILDS D69.010)
ICD-9 287.0
DiseasesDB 5705
MedlinePlus 000425
MeSH D011695

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor-In-Chief: Lakshmi Gopalakrishnan, M.B.B.S.

Overview

Henoch-Schonlein purpura is a disease that involves purple spots on the skin, joint pain, gastrointestinal problems, and glomerulonephritis (a type of kidney disorder).

What are the symptoms of Henoch-Schönlein purpura?

What causes Henoch-Schönlein purpura?

  • Henoch-Schonlein is caused by an abnormal response of the immune system. It is unclear why this occurs.
  • The syndrome is usually seen in children, but it may affect people of any age. It is more common in boys than in girls. Many people with Henoch-Schonlein purpura had an upper respiratory illness in the weeks before.

How to know you have a Henoch-Schönlein purpura?

  • The doctor will examine your body and look at your skin. The physical exam will reveal skin sores (lesions) and joint tenderness.
  • Tests may include:
  • Skin biopsy
  • Urinalysis

When to seek urgent medical care

Call for an appointment with your health care provider if:

  • You develop symptoms of Henoch-Schonlein purpura, particularly if they last for more than a few days
  • You have low urine output after an episode of Henoch-Schonlein purpura

Treatment options

There is no specific treatment. Most cases go away on their own without treatment. If symptoms persist, your doctor may recommend therapy with corticosteroids such as prednisone.

Where to find medical care for Henoch-Schönlein purpura

Directions to Hospitals Treating Henoch-Schönlein purpura

What to expect (Outlook/Prognosis)

The disease usually gets better on its own without treatment.

Possible complications

  • Bleeding inside the body
  • Kidney problems (in rare cases)

Sources

http://www.nlm.nih.gov/medlineplus/ency/article/000425.htm

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