Ectopia cordis

Revision as of 02:06, 9 August 2012 by WikiBot (talk | contribs) (Bot: Automated text replacement (-{{SIB}} + & -{{EJ}} + & -{{EH}} + & -{{Editor Join}} + & -{{Editor Help}} +))
(diff) ← Older revision | Latest revision (diff) | Newer revision → (diff)
Jump to navigation Jump to search
Ectopia cordis

WikiDoc Resources for Ectopia cordis


Most recent articles on Ectopia cordis

Most cited articles on Ectopia cordis

Review articles on Ectopia cordis

Articles on Ectopia cordis in N Eng J Med, Lancet, BMJ


Powerpoint slides on Ectopia cordis

Images of Ectopia cordis

Photos of Ectopia cordis

Podcasts & MP3s on Ectopia cordis

Videos on Ectopia cordis

Evidence Based Medicine

Cochrane Collaboration on Ectopia cordis

Bandolier on Ectopia cordis

TRIP on Ectopia cordis

Clinical Trials

Ongoing Trials on Ectopia cordis at Clinical

Trial results on Ectopia cordis

Clinical Trials on Ectopia cordis at Google

Guidelines / Policies / Govt

US National Guidelines Clearinghouse on Ectopia cordis

NICE Guidance on Ectopia cordis


FDA on Ectopia cordis

CDC on Ectopia cordis


Books on Ectopia cordis


Ectopia cordis in the news

Be alerted to news on Ectopia cordis

News trends on Ectopia cordis


Blogs on Ectopia cordis


Definitions of Ectopia cordis

Patient Resources / Community

Patient resources on Ectopia cordis

Discussion groups on Ectopia cordis

Patient Handouts on Ectopia cordis

Directions to Hospitals Treating Ectopia cordis

Risk calculators and risk factors for Ectopia cordis

Healthcare Provider Resources

Symptoms of Ectopia cordis

Causes & Risk Factors for Ectopia cordis

Diagnostic studies for Ectopia cordis

Treatment of Ectopia cordis

Continuing Medical Education (CME)

CME Programs on Ectopia cordis


Ectopia cordis en Espanol

Ectopia cordis en Francais


Ectopia cordis in the Marketplace

Patents on Ectopia cordis

Experimental / Informatics

List of terms related to Ectopia cordis

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Ectopia cordis is a birth defect in which the heart is abnormally located. In the most common form, the heart protrudes outside the chest through a split sternum. Less often the heart may be situated in the abdominal cavity or neck.

Often other birth defects are also present. This condition is usually fatal in the first days of life. In some cases surgical treatment is possible. The ectopic heart is not protected by the skin or sternum.

Other organs may also have formed outside the skin. Often the heart is not formed properly and many other heart defects are associated with this condition including: Tetralogy of Fallot, pulmonary atresia, atrial and ventricular septal defects, double outlet right ventricle.

Other non cardiac malformations may be present such as cleft palate, spine malformations that can cause kyphosis.


7.9 per million births. Ectopia cordis is a very rare congenital heart malformation.


No exact cause has been identified but this condition has also been seen more frequently in Turner Syndrome and Trisomy 18; however so far there is no evidence that it is a genetically transmissible disease.


Most cases result in stillbirth or death shortly after birth. Some cases of ectopia cordis can be treated surgically but in general involve lengthy and very complicated pediatric cardiothoracic surgery.

Depending on the position of the heart from birth ectopia cordis can be classified into four different categories:

  • Cervical
  • Thoracic: where the heart would lie within the thoracic cavity.
  • Thoracoabdominal: where the heart would lie somewhere between the thoracic and abdominal cavities.
  • Abdominal: where the heart would lie in the abdominal cavity.

The malfunction happens when the sternum forms during the gestation period and the heart begins to grow in the wrong place.


  • Amato J, Douglas W, Desai U, Burke S (2000). "Ectopia cordis". Chest Surg Clin N Am. 10 (2): 297–316, vii. PMID 10803335.
  • Ellis-Christensen, Tricia. "Ectopia cordis".

See also

External Links

Template:WikiDoc Sources