Arrhythmogenic right ventricular dysplasia epidemiology and demographics

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Arrhythmogenic right ventricular dysplasia Microchapters

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Overview

Historical Perspective

Classification

Pathophysiology

Causes

Differentiating Arrhythmogenic right ventricular dysplasia from other Diseases

Epidemiology and Demographics

Risk Factors

Screening

Natural History, Complications and Prognosis

Diagnosis

Diagnostic Criteria

History and Symptoms

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Endomyocardial biopsy

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Overview

ARVD is a rare disease. It is observed more commonly in males, and accounts for 17% of all sudden cardiac deaths in the young.

Epidemiology and demographics

Incidence

Gender

Male to female ratio of 3:1

References

  1. Lahtinen AM, Lehtonen E, Marjamaa A, Kaartinen M, Heliö T, Porthan K; et al. (2011). "Population-prevalent desmosomal mutations predisposing to arrhythmogenic right ventricular cardiomyopathy". Heart Rhythm. 8 (8): 1214–21. doi:10.1016/j.hrthm.2011.03.015. PMID 21397041.
  2. Peters S, Trümmel M, Meyners W (2004). "Prevalence of right ventricular dysplasia-cardiomyopathy in a non-referral hospital". Int J Cardiol. 97 (3): 499–501. doi:10.1016/j.ijcard.2003.10.037. PMID 15561339.

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