Obliterative portal venopathy
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Synonyms and keywords: Hepatoportal sclerosis
Overview
Hepatoportal sclerosis (HPS) is a rare disorder characterized by sclerosis of the intrahepatic portal veins.
Pathophysiology
Pathology
Causes
- Exposure to toxic substances (arsenic or vinyl chloride)
- autoimmune and connective tissue diseases
- systemic or intra abdominal infections
- Clotting factor abnormalities
Differentiating from other Diseases
Epidemiology and Demographics
The prevalence of this disease is unknown, and the distribution is worldwide, with many cases reported in Asia.
Age
The disease can occur at any age.
Gender
Both males and females are equally affected.