Hirschprung disease here classification

Template:Hirschprung disease Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Ahmed Younes M.B.B.CH [2]

Classification

Based on the extent of colon involvement Hirschsprung's disease can be classified into the following:

• Rectosigmoid form: It is the most common form and is seen in 80 to 75% of infants diagnosed with Hirschsprung's disease.
• Long segment colonic Hirschsprung disease: also known as total colonic aganglionosis with ileal involvement upto 50 cm proximal to the ileocecal junction. It is uncommon and accounts for 5 to 7% of cases diagnosed with Hirschsprung's disease.
• Ultra short segment Hirschsprung's disease: Only the internal anal sphincter is affected and is called as internal anal sphincter achalasia.