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'''Contributors:'''  [[User:zorkun|Cafer Zorkun]] M.D., PhD.
'''Contributors:'''  [[User:zorkun|Cafer Zorkun]] M.D., PhD.


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'''Synonyms and Related Keywords:''' Abdominal cocoon, sclerosing peritonitis, encapsulating peritonitis, peritonitis chronica fibrosa incapsulata. <ref>Mustafa Kemal Demir, Okan Akinci, Ender Onur, and Neset Koksal. [http://radiology.rsnajnls.org/cgi/content/full/242/3/937 Case 108: Sclerosing Encapsulating Peritonitis.] Radiology 2007 242: 937-939.</ref>
'''Synonyms and Related Keywords:''' Abdominal cocoon, sclerosing peritonitis, encapsulating peritonitis, peritonitis chronica fibrosa incapsulata. <ref>Mustafa Kemal Demir, Okan Akinci, Ender Onur, and Neset Koksal. [http://radiology.rsnajnls.org/cgi/content/full/242/3/937 Case 108: Sclerosing Encapsulating Peritonitis.] Radiology 2007 242: 937-939.</ref>
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{{Gastroenterology}}
{{Gastroenterology}}
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[[Category:Gastroenterology]]
[[Category:Gastroenterology]]

Revision as of 15:55, 20 August 2012

Sclerosing encapsulating peritonitis
Sclerosing encapsulating peritonitis.
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Contributors: Cafer Zorkun M.D., PhD.


Synonyms and Related Keywords: Abdominal cocoon, sclerosing peritonitis, encapsulating peritonitis, peritonitis chronica fibrosa incapsulata. [1]

Overview

Sclerosing encapsulating peritonitis (SEP) is a rare benign cause of acute or subacute small bowel obstruction. It is characterized by total or partial encasement of the small bowel within a thick fibrocollagenous membrane.

Etiology

Differential Diagnosis

Sclerosing encapsulating peritonitis may be confused with congenital peritoneal encapsulation, which is characterized by a thin accessory peritoneal sac surrounding the small bowel. This asymptomtic condition is generally found incidentally during unrelated surgery and does not fit with the clinical or imaging findings in this group of patients.

Diagnosis

  • Radiographs of the abdomen can show air-fluid levels similar to those in patients with any other cause of small-bowel obstruction.
  • In the appropriate clinical setting, recognition of the entire dilated small bowel at the center of the abdomen and encased within a thick fibrocollageneous membrane, as though it were in a cocoon, on a CT image is diagnostic of sclerosing encapsulating peritonitis.
  • The other imaging findings may include signs of obstruction, fixation of intestinal loops, ascites or localized fluid collections, bowel wall thickening, peritoneal or mural calcification, and reactive adenopathy.

Diagnostic Findings

Patient #1:

CT and gross pathological images demonstrate sclerosing encapsulating peritonitis. The patient was on long term peritoneal dialysis

Images courtesy of RadsWiki

References

  1. Mustafa Kemal Demir, Okan Akinci, Ender Onur, and Neset Koksal. Case 108: Sclerosing Encapsulating Peritonitis. Radiology 2007 242: 937-939.

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