Hemophagocytic lymphohistiocytosis: Difference between revisions

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==[[Hemophagocytic lymphohistiocytosis overview|Overview]]==
==[[Hemophagocytic lymphohistiocytosis overview|Overview]]==
==[[Hemophagocytic lymphohistiocytosis historical perspective|Historical Perspective]]==
==[[Hemophagocytic lymphohistiocytosis classification|Classification]]==
==[[Hemophagocytic lymphohistiocytosis classification|Classification]]==
==[[Hemophagocytic lymphohistiocytosis pathophysiology |Pathophysiology]]==
==[[Hemophagocytic lymphohistiocytosis pathophysiology |Pathophysiology]]==
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==[[Hemophagocytic lymphohistiocytosis differential diagnosis|Differentiating Hemophagocytic lymphohistiocytosis from other Diseases]]==
==[[Hemophagocytic lymphohistiocytosis differential diagnosis|Differentiating Hemophagocytic lymphohistiocytosis from other Diseases]]==
==[[Hemophagocytic lymphohistiocytosis epidemiology and demographics|Epidemiology and Demographics]]==
==[[Hemophagocytic lymphohistiocytosis epidemiology and demographics|Epidemiology and Demographics]]==
==[[Hemophagocytic lymphohistiocytosis risk factors|Risk Factors]]==
==[[Hemophagocytic lymphohistiocytosis screening|Screening]]==
==[[Hemophagocytic lymphohistiocytosis natural history, complications and prognosis|Natural History, Complications and Prognosis]]==
==[[Hemophagocytic lymphohistiocytosis natural history, complications and prognosis|Natural History, Complications and Prognosis]]==
==Diagnosis==
==Diagnosis==
[[Hemophagocytic lymphohistiocytosis history and symptoms|History and Symptoms]] | [[Hemophagocytic lymphohistiocytosis physical examination|Physical Examination]] | [[Hemophagocytic lymphohistiocytosis laboratory findings|Laboratory Findings]] | [[Hemophagocytic lymphohistiocytosis other diagnostic studies|Other Diagnostic Studies]]
[[Hemophagocytic lymphohistiocytosis history and symptoms|History and Symptoms]] | [[Hemophagocytic lymphohistiocytosis physical examination|Physical Examination]] | [[Hemophagocytic lymphohistiocytosis laboratory findings|Laboratory Findings]] | [[Hemophagocytic lymphohistiocytosis x ray|X Ray]] | [[Hemophagocytic lymphohistiocytosis CT|CT]] | [[Hemophagocytic lymphohistiocytosis MRI|MRI]] | [[Hemophagocytic lymphohistiocytosis other imaging findings|Other Imaging Findings]] | [[Hemophagocytic lymphohistiocytosis other diagnostic studies|Other Diagnostic Studies]]


==Treatment==
==Treatment==
[[Hemophagocytic lymphohistiocytosis medical therapy|Medical Therapy]] | [[Hemophagocytic lymphohistiocytosis surgery|Surgery]] | [[Hemophagocytic lymphohistiocytosis cost-effectiveness of therapy|Cost-Effectiveness of Therapy]] | [[Hemophagocytic lymphohistiocytosis future or investigational therapies|Future or Investigational Therapies]]
[[Hemophagocytic lymphohistiocytosis medical therapy|Medical Therapy]] | [[Hemophagocytic lymphohistiocytosis surgery|Surgery]] | [[Hemophagocytic lymphohistiocytosis primary prevention|Primary Prevention]] | [[Hemophagocytic lymphohistiocytosis Secondary Prevention|Secondary Prevention]] | [[Hemophagocytic lymphohistiocytosis cost-effectiveness of therapy|Cost-Effectiveness of Therapy]] | [[Hemophagocytic lymphohistiocytosis future or investigational therapies|Future or Investigational Therapies]]
==Case Studies==
==Case Studies==
[[Hemophagocytic lymphohistiocytosis case study one|Case #1]]
[[Hemophagocytic lymphohistiocytosis case study one|Case #1]]
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{{Hematology}}
{{Hematology}}


[[Category:Disease]]
 
[[Category:Pediatrics]]
[[Category:Pediatrics]]
[[Category:Hematology]]
[[Category:Hematology]]
[[Category:Blood disorders]]
 
[[Category:Genetic disorders]]
[[Category:Autosomal recessive disorders]]


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Latest revision as of 13:03, 23 June 2016

Hemophagocytic lymphohistiocytosis
Light microscopic image of bone marrow showing stromal macrophages containing numerous red blood cells in their cytoplasm
ICD-10 D76.1
ICD-9 288.4
OMIM 267700 603552
DiseasesDB 31418
MeSH D051359

Hemophagocytic lymphohistiocytosis Microchapters

Home

Overview

Historical Perspective

Classification

Pathophysiology

Causes

Differentiating Hemophagocytic lymphohistiocytosis from other Diseases

Epidemiology and Demographics

Risk Factors

Screening

Natural History, Complications and Prognosis

Diagnosis

History and Symptoms

Physical Examination

Laboratory Findings

X Ray

CT

MRI

Other Imaging Findings

Other Diagnostic Studies

Treatment

Medical Therapy

Surgery

Primary Prevention

Secondary Prevention

Cost-Effectiveness of Therapy

Future or Investigational Therapies

Case Studies

Case #1

Hemophagocytic lymphohistiocytosis On the Web

Most recent articles

Most cited articles

Review articles

CME Programs

Powerpoint slides

Images

American Roentgen Ray Society Images of Hemophagocytic lymphohistiocytosis

All Images
X-rays
Echo & Ultrasound
CT Images
MRI

Ongoing Trials at Clinical Trials.gov

US National Guidelines Clearinghouse

NICE Guidance

FDA on Hemophagocytic lymphohistiocytosis

CDC on Hemophagocytic lymphohistiocytosis

Hemophagocytic lymphohistiocytosis in the news

Blogs on Hemophagocytic lymphohistiocytosis

Directions to Hospitals Treating Hemophagocytic lymphohistiocytosis

Risk calculators and risk factors for Hemophagocytic lymphohistiocytosis

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Raviteja Guddeti, M.B.B.S. [2]

Synonyms and keywords: Hemophagocytic syndrome; familial histiocytic reticulosis; hemophagocytic lymphohistiocytosis - familial; erythrophagocytic lymphohistiocytosis - familial; familial haemophagocytic lymphohistiocytosis; HLH

Overview

Historical Perspective

Classification

Pathophysiology

Causes

Differentiating Hemophagocytic lymphohistiocytosis from other Diseases

Epidemiology and Demographics

Risk Factors

Screening

Natural History, Complications and Prognosis

Diagnosis

History and Symptoms | Physical Examination | Laboratory Findings | X Ray | CT | MRI | Other Imaging Findings | Other Diagnostic Studies

Treatment

Medical Therapy | Surgery | Primary Prevention | Secondary Prevention | Cost-Effectiveness of Therapy | Future or Investigational Therapies

Case Studies

Case #1

Template:Hematology


Template:WikiDoc Sources