Acrania

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Acrania
ICD-10 Q00.0
ICD-9 740.0

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Overview

Acrania is a cephalic disorder of a human fetus characterised by a partial or complete absence of the cranium. The condition is frequently, though not always, associated with anencephaly. [1]

Diagnosis

Ultrasound can be involved in diagnosis.[2]

Prognosis

Whether diagnosed during pregnancy or at birth, the condition is invariably fatal.[1]

References

  1. 1.0 1.1 Acrania: review of 13 cases - Tae-Hee Kwon, MD*, Jim King, MD, Philippe Jeanty, MD, PhD
  2. Liu IF, Chang CH, Yu CH, Cheng YC, Chang FM (2005). "Prenatal diagnosis of fetal acrania using three-dimensional ultrasound". Ultrasound in medicine & biology. 31 (2): 175–8. doi:10.1016/j.ultrasmedbio.2004.10.005. PMID 15708455.

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